| Year |
Citation |
Score |
| 2022 |
Luttik K, Tejwani L, Ju H, Driessen T, Smeets CJLM, Edamakanti CR, Khan A, Yun J, Opal P, Lim J. Differential effects of Wnt-β-catenin signaling in Purkinje cells and Bergmann glia in spinocerebellar ataxia type 1. Proceedings of the National Academy of Sciences of the United States of America. 119: e2208513119. PMID 35969780 DOI: 10.1073/pnas.2208513119 |
0.637 |
|
| 2020 |
Edamakanti CR, Opal P. Purification of Prominin-1+ Stem Cells from Postnatal Mouse Cerebellum. Journal of Visualized Experiments : Jove. PMID 32338650 DOI: 10.3791/60554 |
0.338 |
|
| 2019 |
Didonna A, Opal P. The role of neurofilament aggregation in neurodegeneration: lessons from rare inherited neurological disorders. Molecular Neurodegeneration. 14: 19. PMID 31097008 DOI: 10.1186/s13024-019-0318-4 |
0.388 |
|
| 2019 |
Hu YS, Do J, Edamakanti CR, Kini AR, Martina M, Stupp SI, Opal P. Self-assembling vascular endothelial growth factor nanoparticles improve function in spinocerebellar ataxia type 1. Brain : a Journal of Neurology. PMID 30649233 DOI: 10.1093/Brain/Awy328 |
0.313 |
|
| 2018 |
Frederick NM, Shah PV, Didonna A, Langley MR, Kanthasamy AG, Opal P. Loss of the dystonia gene Thap1 leads to transcriptional deficits that converge on common pathogenic pathways in dystonic syndromes. Human Molecular Genetics. PMID 30590536 DOI: 10.1093/Hmg/Ddy433 |
0.402 |
|
| 2018 |
Murmann AE, Yu J, Opal P, Peter ME. Trinucleotide Repeat Expansion Diseases, RNAi, and Cancer. Trends in Cancer. 4: 684-700. PMID 30292352 DOI: 10.1016/J.Trecan.2018.08.004 |
0.367 |
|
| 2018 |
Edamakanti CR, Do J, Didonna A, Martina M, Opal P. Mutant ataxin1 disrupts cerebellar development in spinocerebellar ataxia type 1. The Journal of Clinical Investigation. PMID 29533923 DOI: 10.1172/Jci96765 |
0.431 |
|
| 2018 |
Yang X, Lu B, Sun X, Han C, Fu C, Xu K, Wang M, Li D, Chen Z, Opal P, Wen Q, Crispino JD, Wang QF, Huang Z. ANP32A regulates histone H3 acetylation and promotes leukemogenesis. Leukemia. PMID 29467488 DOI: 10.1038/S41375-018-0010-7 |
0.391 |
|
| 2016 |
Lin NH, Huang YS, Opal P, Goldman RD, Messing A, Perng MD. The role of gigaxonin in the degradation of the glial-specific intermediate filament protein GFAP. Molecular Biology of the Cell. PMID 27798231 DOI: 10.1091/Mbc.E16-06-0362 |
0.433 |
|
| 2016 |
Didonna A, Opal P. Advances in Sequencing Technologies for Understanding Hereditary Ataxias: A Review. Jama Neurology. PMID 27749953 DOI: 10.1001/jamaneurol.2016.3097 |
0.3 |
|
| 2016 |
Venkatraman A, Opal P. Paraneoplastic cerebellar degeneration with anti-Yo antibodies - a review. Annals of Clinical and Translational Neurology. 3: 655-63. PMID 27606347 DOI: 10.1002/acn3.328 |
0.312 |
|
| 2016 |
Cvetanovic M, Hu YS, Opal P. Mutant Ataxin-1 Inhibits Neural Progenitor Cell Proliferation in SCA1. Cerebellum (London, England). PMID 27306906 DOI: 10.1007/S12311-016-0794-9 |
0.685 |
|
| 2016 |
Israeli E, Dryanovski DI, Schumacker PT, Chandel NS, Singer JD, Julien JP, Goldman RD, Opal P. Intermediate filament aggregates cause mitochondrial dysmotility and increase energy demands in Giant Axonal Neuropathy. Human Molecular Genetics. PMID 27000625 DOI: 10.1093/Hmg/Ddw081 |
0.386 |
|
| 2015 |
Lowery J, Jain N, Kuczmarski ER, Mahammad S, Goldman A, Gelfand VI, Opal P, Goldman RD. Abnormal Intermediate Filament Organization Alters Mitochondrial Motility in Giant Axonal Neuropathy Fibroblasts. Molecular Biology of the Cell. PMID 26700320 DOI: 10.1091/Mbc.E15-09-0627 |
0.328 |
|
| 2015 |
Dell'Orco JM, Wasserman AH, Chopra R, Ingram MA, Hu YS, Singh V, Wulff H, Opal P, Orr HT, Shakkottai VG. Neuronal Atrophy Early in Degenerative Ataxia Is a Compensatory Mechanism to Regulate Membrane Excitability. The Journal of Neuroscience : the Official Journal of the Society For Neuroscience. 35: 11292-307. PMID 26269637 DOI: 10.1523/Jneurosci.1357-15.2015 |
0.359 |
|
| 2015 |
Didonna A, Opal P. The promise and perils of HDAC inhibitors in neurodegeneration. Annals of Clinical and Translational Neurology. 2: 79-101. PMID 25642438 DOI: 10.1002/acn3.147 |
0.384 |
|
| 2015 |
Cvetanovic M, Ingram M, Orr H, Opal P. Early activation of microglia and astrocytes in mouse models of spinocerebellar ataxia type 1. Neuroscience. 289: 289-99. PMID 25595967 DOI: 10.1016/J.Neuroscience.2015.01.003 |
0.675 |
|
| 2014 |
Venkatraman A, Hu YS, Didonna A, Cvetanovic M, Krbanjevic A, Bilesimo P, Opal P. The histone deacetylase HDAC3 is essential for Purkinje cell function, potentially complicating the use of HDAC inhibitors in SCA1. Human Molecular Genetics. 23: 3733-45. PMID 24594842 DOI: 10.1093/Hmg/Ddu081 |
0.703 |
|
| 2013 |
Mahammad S, Murthy SN, Didonna A, Grin B, Israeli E, Perrot R, Bomont P, Julien JP, Kuczmarski E, Opal P, Goldman RD. Giant axonal neuropathy-associated gigaxonin mutations impair intermediate filament protein degradation. The Journal of Clinical Investigation. 123: 1964-75. PMID 23585478 DOI: 10.1172/Jci66387 |
0.415 |
|
| 2013 |
Opal P, Zoghbi H. The Hereditary Ataxias Emery and Rimoin's Principles and Practice of Medical Genetics. 1-32. DOI: 10.1016/B978-0-12-383834-6.00125-7 |
0.41 |
|
| 2012 |
Cvetanovic M, Kular RK, Opal P. LANP mediates neuritic pathology in Spinocerebellar ataxia type 1. Neurobiology of Disease. 48: 526-32. PMID 22884877 DOI: 10.1016/J.Nbd.2012.07.024 |
0.707 |
|
| 2011 |
Cvetanovic M, Patel JM, Marti HH, Kini AR, Opal P. Vascular endothelial growth factor ameliorates the ataxic phenotype in a mouse model of spinocerebellar ataxia type 1. Nature Medicine. 17: 1445-7. PMID 22001907 DOI: 10.1038/Nm.2494 |
0.655 |
|
| 2010 |
Kular RK, Gogliotti RG, Opal P. Cpd-1 null mice display a subtle neurological phenotype. Plos One. 5. PMID 20844742 DOI: 10.1371/Journal.Pone.0012649 |
0.388 |
|
| 2009 |
Kular RK, Cvetanovic M, Siferd S, Kini AR, Opal P. Neuronal differentiation is regulated by leucine-rich acidic nuclear protein (LANP), a member of the inhibitor of histone acetyltransferase complex. The Journal of Biological Chemistry. 284: 7783-92. PMID 19136565 DOI: 10.1074/Jbc.M806150200 |
0.694 |
|
| 2007 |
Cvetanovic M, Rooney RJ, Garcia JJ, Toporovskaya N, Zoghbi HY, Opal P. The role of LANP and ataxin 1 in E4F-mediated transcriptional repression. Embo Reports. 8: 671-7. PMID 17557114 DOI: 10.1038/Sj.Embor.7400983 |
0.71 |
|
| 2007 |
Paganoni S, Naidech AM, Opal P. Huntington's disease presenting as postsurgical psychosis. Movement Disorders : Official Journal of the Movement Disorder Society. 22: 1209-10. PMID 17443707 DOI: 10.1002/Mds.21522 |
0.307 |
|
| 2004 |
Opal P, Garcia JJ, McCall AE, Xu B, Weeber EJ, Sweatt JD, Orr HT, Zoghbi HY. Generation and characterization of LANP/pp32 null mice. Molecular and Cellular Biology. 24: 3140-9. PMID 15060138 DOI: 10.1128/Mcb.24.8.3140-3149.2004 |
0.554 |
|
| 2003 |
Opal P, Garcia JJ, Propst F, Matilla A, Orr HT, Zoghbi HY. Mapmodulin/leucine-rich acidic nuclear protein binds the light chain of microtubule-associated protein 1B and modulates neuritogenesis. The Journal of Biological Chemistry. 278: 34691-9. PMID 12807913 DOI: 10.1074/Jbc.M302785200 |
0.569 |
|
| 2002 |
Opal P, Zoghbi HY. The role of chaperones in polyglutamine disease. Trends in Molecular Medicine. 8: 232-6. PMID 12067633 DOI: 10.1016/S1471-4914(02)02310-9 |
0.561 |
|
| 2001 |
Cummings CJ, Sun Y, Opal P, Antalffy B, Mestril R, Orr HT, Dillmann WH, Zoghbi HY. Over-expression of inducible HSP70 chaperone suppresses neuropathology and improves motor function in SCA1 mice. Human Molecular Genetics. 10: 1511-8. PMID 11448943 DOI: 10.1093/Hmg/10.14.1511 |
0.595 |
|
| Low-probability matches (unlikely to be authored by this person) |
| 2007 |
Bassuk AG, Chen YZ, Batish SD, Nagan N, Opal P, Chance PF, Bennett CL. In cis autosomal dominant mutation of Senataxin associated with tremor/ataxia syndrome. Neurogenetics. 8: 45-9. PMID 17096168 DOI: 10.1007/s10048-006-0067-8 |
0.3 |
|
| 2008 |
Paganoni S, Seelaus CA, Ormond KE, Opal P. Association of spinocerebellar ataxia type 3 and spinocerebellar ataxia type 8 microsatellite expansions: genetic counseling implications. Movement Disorders : Official Journal of the Movement Disorder Society. 23: 154-5. PMID 17987652 DOI: 10.1002/Mds.21797 |
0.298 |
|
| 2023 |
Edamakanti CR, Mohan V, Opal P. Reactive Bergmann glia play a central role in spinocerebellar ataxia inflammation via the JNK pathway. Journal of Neuroinflammation. 20: 126. PMID 37237366 DOI: 10.1186/s12974-023-02801-1 |
0.295 |
|
| 2013 |
Opal P, Goldman RD. Explaining intermediate filament accumulation in giant axonal neuropathy. Rare Diseases (Austin, Tex.). 1: e25378. PMID 25003002 DOI: 10.4161/rdis.25378 |
0.289 |
|
| 1992 |
Eriksson JE, Opal P, Goldman RD. Intermediate filament dynamics. Current Opinion in Cell Biology. 4: 99-104. PMID 1558758 DOI: 10.1016/0955-0674(92)90065-K |
0.282 |
|
| 2002 |
Opal P, Tintner R, Jankovic J, Leung J, Breakefield XO, Friedman J, Ozelius L. Intrafamilial phenotypic variability of the DYT1 dystonia: from asymptomatic TOR1A gene carrier status to dystonic storm. Movement Disorders : Official Journal of the Movement Disorder Society. 17: 339-45. PMID 11921121 DOI: 10.1002/mds.10096 |
0.281 |
|
| 1996 |
Goldman RD, Khuon S, Chou YH, Opal P, Steinert PM. The function of intermediate filaments in cell shape and cytoskeletal integrity. The Journal of Cell Biology. 134: 971-83. PMID 8769421 DOI: 10.1083/Jcb.134.4.971 |
0.273 |
|
| 1996 |
Straube-West K, Loomis PA, Opal P, Goldman RD. Alterations in neural intermediate filament organization: functional implications and the induction of pathological changes related to motor neuron disease. Journal of Cell Science. 109: 2319-29. PMID 8886982 |
0.268 |
|
| 2023 |
Battaglia R, Faridounnia M, Beltran A, Robinson J, Kinghorn K, Ezzell JA, Bharucha-Goebel D, Bonnemann C, Hooper JE, Opal P, Bouldin TW, Armao D, Snider N. Intermediate filament dysregulation in astrocytes in the human disease model of mutation in giant axonal neuropathy (GAN). Molecular Biology of the Cell. mbcE23030094. PMID 37672338 DOI: 10.1091/mbc.E23-03-0094 |
0.242 |
|
| 1991 |
Goldman RD, Chou YH, Dessev C, Dessev G, Eriksson J, Goldman A, Khuon S, Kohnken R, Lowy M, Miller R, Murphy K, Opal P, Skalli O, Straube K. Dynamic aspects of cytoskeletal and karyoskeletal intermediate filament systems during the cell cycle Cold Spring Harbor Symposia On Quantitative Biology. 56: 629-642. PMID 1819512 DOI: 10.1101/Sqb.1991.056.01.072 |
0.24 |
|
| 2023 |
Battaglia R, Faridounnia M, Beltran A, Robinson J, Kinghorn K, Ezzell JA, Bharucha-Goebel D, Bonnemann C, Hooper JE, Opal P, Bouldin TW, Armao D, Snider N. Intermediate filament dysregulation and astrocytopathy in the human disease model of mutation in giant axonal neuropathy (GAN). Biorxiv : the Preprint Server For Biology. PMID 36993491 DOI: 10.1101/2023.03.13.532440 |
0.238 |
|
| 2023 |
Renganathan B, Zewe JP, Cheng Y, Paumier JM, Kittisopikul M, Ridge KM, Opal P, Gelfand VI. Gigaxonin is required for intermediate filament transport. Faseb Journal : Official Publication of the Federation of American Societies For Experimental Biology. 37: e22886. PMID 37043392 DOI: 10.1096/fj.202202119R |
0.228 |
|
| 1998 |
Opal P, Paulson H. Genetic Instabilities and Hereditary Neurological Diseases The American Journal of Human Genetics. 63: 1921. DOI: 10.1086/302134 |
0.225 |
|
| 2015 |
Rozenfeld MN, Nemeth AJ, Walker MT, Mohan P, Wang X, Parrish TB, Opal P. An investigation of diffusion imaging techniques in the evaluation of spinocerebellar ataxia and multisystem atrophy. Journal of Clinical Neuroscience : Official Journal of the Neurosurgical Society of Australasia. 22: 166-72. PMID 25439745 DOI: 10.1016/j.jocn.2014.08.006 |
0.222 |
|
| 2024 |
Sekerková G, Kiliç S, Cheng YH, Fredrick N, Osmani A, Kim H, Opal P, Martina M. Phenotypical, genotypical and pathological characterization of the moonwalker mouse, a model of ataxia. Neurobiology of Disease. 106492. PMID 38575093 DOI: 10.1016/j.nbd.2024.106492 |
0.219 |
|
| 2017 |
Sun X, Lu B, Han C, Qiu W, Jin Q, Li D, Li Q, Yang Q, Wen Q, Opal P, Kini AR, Crispino JD, Huang Z. ANP32A dysregulation contributes to abnormal megakaryopoiesis in acute megakaryoblastic leukemia. Blood Cancer Journal. 7: 661. PMID 29269781 DOI: 10.1038/S41408-017-0031-X |
0.211 |
|
| 2021 |
Edamakanti CR, Opal P. Developmental Alterations in Adult-Onset Neurodegenerative Disorders: Lessons from Polyglutamine Diseases. Movement Disorders : Official Journal of the Movement Disorder Society. PMID 34014004 DOI: 10.1002/mds.28657 |
0.209 |
|
| 2021 |
Frederick NM, Pooler MM, Shah P, Didonna A, Opal P. Pharmacological perturbation reveals deficits in D2 receptor responses in Thap1 null mice. Annals of Clinical and Translational Neurology. 8: 2302-2308. PMID 34802187 DOI: 10.1002/acn3.51481 |
0.208 |
|
| 2023 |
Opal P. Spinocerebellar ataxia type 1: It's not just about Purkinje cells. Neuron. 111: 2461-2462. PMID 37591199 DOI: 10.1016/j.neuron.2023.07.014 |
0.199 |
|
| 2021 |
Chen ML, Lin CC, Rosenthal LS, Opal P, Kuo SH. Rating scales and biomarkers for CAG-repeat spinocerebellar ataxias: Implications for therapy development. Journal of the Neurological Sciences. 424: 117417. PMID 33836316 DOI: 10.1016/j.jns.2021.117417 |
0.185 |
|
| 2022 |
Selvadurai LP, Perlman SL, Wilmot GR, Subramony SH, Gomez CM, Ashizawa T, Paulson HL, Onyike CU, Rosenthal LS, Sair HI, Kuo SH, Ratai EM, Zesiewicz TA, Bushara KO, Öz G, ... ... Opal P, et al. The S-Factor, a New Measure of Disease Severity in Spinocerebellar Ataxia: Findings and Implications. Cerebellum (London, England). PMID 35962273 DOI: 10.1007/s12311-022-01424-1 |
0.157 |
|
| 1996 |
Chou YH, Opal P, Quinlan RA, Goldman RD. The relative roles of specific N- and C-terminal phosphorylation sites in the disassembly of intermediate filament in mitotic BHK-21 cells. Journal of Cell Science. 109: 817-26. PMID 8718673 |
0.142 |
|
| 2023 |
Santorelli FM, McLoughlin HS, Wolter JM, Galatolo D, Synofzik M, Mengel D, Opal P. Standards of Fluid Biomarker Collection and Pre-analytical Processes in Humans and Mice: Recommendations by the Ataxia Global Initiative Working Group on Biomarkers. Cerebellum (London, England). PMID 37243885 DOI: 10.1007/s12311-023-01561-1 |
0.142 |
|
| 2021 |
Brooker SM, Edamakanti CR, Akasha SM, Kuo SH, Opal P. Spinocerebellar ataxia clinical trials: opportunities and challenges. Annals of Clinical and Translational Neurology. PMID 34019331 DOI: 10.1002/acn3.51370 |
0.141 |
|
| 2020 |
Tan EK, Albanese A, Chaudhuri K, Lim SY, Oey NE, Shan Chan CH, Wu YC, Jeon B, Truong D, Poewe W, Pal PK, Tan L, Opal P, Colosimo C, Jinnah HA, et al. Adapting to post-COVID19 research in Parkinson's disease: Lessons from a multinational experience. Parkinsonism & Related Disorders. PMID 33071183 DOI: 10.1016/j.parkreldis.2020.10.009 |
0.139 |
|
| 2014 |
Opal P, Orr HT. Animal Models of Spinocerebellar Ataxia Type 1 Movement Disorders: Genetics and Models: Second Edition. 979-990. DOI: 10.1016/B978-0-12-405195-9.00063-9 |
0.129 |
|
| 2024 |
Selvadurai LP, Perlman SL, Ashizawa T, Wilmot GR, Onyike CU, Rosenthal LS, Shakkottai VG, Paulson HL, Subramony SH, Bushara KO, Kuo SH, Dietiker C, Geschwind MD, Nelson AB, Gomez CM, ... Opal P, et al. The Cerebellar Cognitive Affective/Schmahmann Syndrome Scale in Spinocerebellar Ataxias. Cerebellum (London, England). PMID 38165578 DOI: 10.1007/s12311-023-01651-0 |
0.119 |
|
| 2024 |
Lin CR, Kuo SH, Opal P. Cognitive, Emotional, and Other Non-motor Symptoms of Spinocerebellar Ataxias. Current Neurology and Neuroscience Reports. PMID 38270820 DOI: 10.1007/s11910-024-01331-4 |
0.111 |
|
| 2024 |
Lai RY, Rummey C, Amlang CJ, Lin CR, Chen TX, Perlman S, Wilmot G, Gomez CM, Schmahmann JD, Paulson H, Ying SH, Onyike CU, Zesiewicz TA, Bushara KO, Geschwind MD, ... ... Opal P, et al. Fatigue Impacts Quality of Life in People with Spinocerebellar Ataxias. Movement Disorders Clinical Practice. PMID 38419568 DOI: 10.1002/mdc3.14006 |
0.071 |
|
| 2022 |
Cao TQ, Harris GR, Lineback CM, Sokol LL, Mencacci N, Opal P. Clinical Reasoning: A 77-Year-Old Man With Involuntary Movements, Sleep Changes, Falls, Bulbar Symptoms, and Cognitive Complaints. Neurology. PMID 35487699 DOI: 10.1212/WNL.0000000000200705 |
0.045 |
|
| 2020 |
Tan EK, Albanese A, Chaudhuri KR, Opal P, Wu YC, Chan CH, Jeon B, Truong D, Poewe W, Tan L, Pal P, Colosimo C, Lim SY, Jinnah HA, Cardoso F. Neurological research & training after the easing of lockdown in countries impacted by COVID-19. Journal of the Neurological Sciences. 418: 117105. PMID 32980781 DOI: 10.1016/j.jns.2020.117105 |
0.017 |
|
| Hide low-probability matches. |