| Year |
Citation |
Score |
| 2008 |
Grubb JH, Vogler C, Levy B, Galvin N, Tan Y, Sly WS. Chemically modified beta-glucuronidase crosses blood-brain barrier and clears neuronal storage in murine mucopolysaccharidosis VII. Proceedings of the National Academy of Sciences of the United States of America. 105: 2616-21. PMID 18268347 DOI: 10.1073/Pnas.0712147105 |
0.353 |
|
| 2008 |
Galvin N, Vogler C, Levy B, Kovacs A, Griffey M, Sands MS. A murine model of infantile neuronal ceroid lipofuscinosis-ultrastructural evaluation of storage in the central nervous system and viscera. Pediatric and Developmental Pathology : the Official Journal of the Society For Pediatric Pathology and the Paediatric Pathology Society. 11: 185-92. PMID 17990914 DOI: 10.2350/07-03-0242.1 |
0.368 |
|
| 2007 |
Dickson P, McEntee M, Vogler C, Le S, Levy B, Peinovich M, Hanson S, Passage M, Kakkis E. Intrathecal enzyme replacement therapy: successful treatment of brain disease via the cerebrospinal fluid. Molecular Genetics and Metabolism. 91: 61-8. PMID 17321776 DOI: 10.1016/J.Ymgme.2006.12.012 |
0.349 |
|
| 2007 |
Donsante A, Levy B, Vogler C, Sands MS. Clinical response to persistent, low-level beta-glucuronidase expression in the murine model of mucopolysaccharidosis type VII. Journal of Inherited Metabolic Disease. 30: 227-38. PMID 17308887 DOI: 10.1007/S10545-007-0483-4 |
0.356 |
|
| 2007 |
Lin D, Donsante A, Macauley S, Levy B, Vogler C, Sands MS. Central nervous system-directed AAV2/5-mediated gene therapy synergizes with bone marrow transplantation in the murine model of globoid-cell leukodystrophy. Molecular Therapy : the Journal of the American Society of Gene Therapy. 15: 44-52. PMID 17164774 DOI: 10.1038/Sj.Mt.6300026 |
0.386 |
|
| 2006 |
Sly WS, Vogler C, Grubb JH, Levy B, Galvin N, Tan Y, Nishioka T, Tomatsu S. Enzyme therapy in mannose receptor-null mucopolysaccharidosis VII mice defines roles for the mannose 6-phosphate and mannose receptors. Proceedings of the National Academy of Sciences of the United States of America. 103: 15172-7. PMID 17015822 DOI: 10.1073/Pnas.0607053103 |
0.368 |
|
| 2006 |
Lessard MD, Alley TL, Proctor JL, Levy B, Galvin N, Vogler CA, Soper BW. Attenuation of murine lysosomal storage disease by allogeneic neonatal bone marrow transplantation using costimulatory blockade and donor lymphocyte infusion without myeloablation. Clinical Immunology (Orlando, Fla.). 119: 166-79. PMID 16487752 DOI: 10.1016/J.Clim.2005.12.015 |
0.324 |
|
| 2005 |
Vogler C, Levy B, Galvin N, Lessard M, Soper B, Barker J. Early onset of lysosomal storage disease in a murine model of mucopolysaccharidosis type VII: undegraded substrate accumulates in many tissues in the fetus and very young MPS VII mouse. Pediatric and Developmental Pathology : the Official Journal of the Society For Pediatric Pathology and the Paediatric Pathology Society. 8: 453-62. PMID 16222480 DOI: 10.1007/S10024-005-0025-8 |
0.419 |
|
| 2005 |
Vogler C, Levy B, Grubb JH, Galvin N, Tan Y, Kakkis E, Pavloff N, Sly WS. Overcoming the blood-brain barrier with high-dose enzyme replacement therapy in murine mucopolysaccharidosis VII. Proceedings of the National Academy of Sciences of the United States of America. 102: 14777-82. PMID 16162667 DOI: 10.1073/Pnas.0506892102 |
0.385 |
|
| 2005 |
Orii KO, Grubb JH, Vogler C, Levy B, Tan Y, Markova K, Davidson BL, Mao Q, Orii T, Kondo N, Sly WS. Defining the pathway for Tat-mediated delivery of beta-glucuronidase in cultured cells and MPS VII mice. Molecular Therapy : the Journal of the American Society of Gene Therapy. 12: 345-52. PMID 16043103 DOI: 10.1016/J.Ymthe.2005.02.031 |
0.326 |
|
| 2005 |
Lin D, Fantz CR, Levy B, Rafi MA, Vogler C, Wenger DA, Sands MS. AAV2/5 vector expressing galactocerebrosidase ameliorates CNS disease in the murine model of globoid-cell leukodystrophy more efficiently than AAV2. Molecular Therapy : the Journal of the American Society of Gene Therapy. 12: 422-30. PMID 15996520 DOI: 10.1016/J.Ymthe.2005.04.019 |
0.377 |
|
| 2005 |
Lin D, Donsante A, Macauley S, Levy B, Vogler C, Sands M. 424. Intracranial AAV5 Synergizes with Non-Myeloablative Bone Marrow Transplantation in the Murine Model of Globoid-Cell Leukodystrophy Molecular Therapy. 11. DOI: 10.1016/J.Ymthe.2005.06.426 |
0.415 |
|
| 2005 |
Donsante A, Levy B, Vogler C, Sands M. 237. Evaluation of Low-Level, Constitutive Expression of |[beta]|-glucuronidase on the Clinical Manifestations of Mucopolysaccharidosis Type VII Molecular Therapy. 11. DOI: 10.1016/J.Ymthe.2005.06.240 |
0.388 |
|
| 2004 |
Kakkis E, McEntee M, Vogler C, Le S, Levy B, Belichenko P, Mobley W, Dickson P, Hanson S, Passage M. Intrathecal enzyme replacement therapy reduces lysosomal storage in the brain and meninges of the canine model of MPS I Molecular Genetics and Metabolism. 83: 163-174. PMID 15464431 DOI: 10.1016/J.Ymgme.2004.07.003 |
0.38 |
|
| 2004 |
Griffey M, Bible E, Vogler C, Levy B, Gupta P, Cooper J, Sands MS. Adeno-associated virus 2-mediated gene therapy decreases autofluorescent storage material and increases brain mass in a murine model of infantile neuronal ceroid lipofuscinosis. Neurobiology of Disease. 16: 360-9. PMID 15193292 DOI: 10.1016/J.Nbd.2004.03.005 |
0.363 |
|
| 2004 |
Soper BW, Duffy TM, Lessard MD, Jude CD, Schuldt AJ, Vogler CA, Levy B, Barker JE. Transplanted ER-MP12hi20-58med/hi myeloid progenitors produce resident macrophages from marrow that are therapeutic for lysosomal storage disease. Blood Cells, Molecules & Diseases. 32: 199-213. PMID 14757436 DOI: 10.1016/J.Bcmd.2003.09.003 |
0.346 |
|
| 2003 |
Tomatsu S, Orii KO, Vogler C, Nakayama J, Levy B, Grubb JH, Gutierrez MA, Shim S, Yamaguchi S, Nishioka T, Montano AM, Noguchi A, Orii T, Kondo N, Sly WS. Mouse model of N-acetylgalactosamine-6-sulfate sulfatase deficiency (Galns-/-) produced by targeted disruption of the gene defective in Morquio A disease. Human Molecular Genetics. 12: 3349-58. PMID 14583446 DOI: 10.1093/Hmg/Ddg366 |
0.412 |
|
| 2003 |
Hennig AK, Levy B, Ogilvie JM, Vogler CA, Galvin N, Bassnett S, Sands MS. Intravitreal gene therapy reduces lysosomal storage in specific areas of the CNS in mucopolysaccharidosis VII mice. The Journal of Neuroscience : the Official Journal of the Society For Neuroscience. 23: 3302-7. PMID 12716937 DOI: 10.1523/Jneurosci.23-08-03302.2003 |
0.397 |
|
| 2003 |
Vogler C, Galvin N, Levy B, Grubb J, Jiang J, Zhou XY, Sly WS. Transgene produces massive overexpression of human beta -glucuronidase in mice, lysosomal storage of enzyme, and strain-dependent tumors. Proceedings of the National Academy of Sciences of the United States of America. 100: 2669-73. PMID 12591953 DOI: 10.1073/Pnas.0437941100 |
0.38 |
|
| 2001 |
Barker JE, Deveau S, Lessard M, Hamblen N, Vogler C, Levy B. In utero fetal liver cell transplantation without toxic irradiation alleviates lysosomal storage in mice with mucopolysaccharidosis type VII. Blood Cells, Molecules & Diseases. 27: 861-73. PMID 11783949 DOI: 10.1006/Bcmd.2001.0453 |
0.382 |
|
| 2001 |
Vogler C, Barker J, Sands MS, Levy B, Galvin N, Sly WS. Murine mucopolysaccharidosis VIL: impact of therapies on the phenotype, clinical course, and pathology in a model of a lysosomal storage disease. Pediatric and Developmental Pathology : the Official Journal of the Society For Pediatric Pathology and the Paediatric Pathology Society. 4: 421-33. PMID 11779044 DOI: 10.1007/S10024001-0079-1 |
0.386 |
|
| 2001 |
Vogler C, Levy B, Galvin N, Sands MS, Birkenmeier EH, Sly WS, Barker J. A novel model of murine mucopolysaccharidosis type VII due to an intracisternal a particle element transposition into the beta-glucuronidase gene: clinical and pathologic findings. Pediatric Research. 49: 342-8. PMID 11228259 DOI: 10.1203/00006450-200103000-00007 |
0.395 |
|
| 2001 |
Soper BW, Lessard MD, Vogler CA, Levy B, Beamer WG, Sly WS, Barker JE. Nonablative neonatal marrow transplantation attenuates functional and physical defects of beta-glucuronidase deficiency. Blood. 97: 1498-504. PMID 11222399 DOI: 10.1182/Blood.V97.5.1498 |
0.385 |
|
| 1999 |
Vogler C, Levy B, Galvin NJ, Thorpe C, Sands MS, Barker JE, Baty J, Birkenmeier EH, Sly WS. Enzyme replacement in murine mucopolysaccharidosis type VII: neuronal and glial response to beta-glucuronidase requires early initiation of enzyme replacement therapy. Pediatric Research. 45: 838-44. PMID 10367775 DOI: 10.1203/00006450-199906000-00010 |
0.41 |
|
| 1999 |
Daly TM, Vogler C, Levy B, Haskins ME, Sands MS. Neonatal gene transfer leads to widespread correction of pathology in a murine model of lysosomal storage disease. Proceedings of the National Academy of Sciences of the United States of America. 96: 2296-300. PMID 10051635 DOI: 10.1073/Pnas.96.5.2296 |
0.404 |
|
| 1998 |
Vogler C, Sands MS, Galvin N, Levy B, Thorpe C, Barker J, Sly WS. Murine mucopolysaccharidosis type VII: the impact of therapies on the clinical course and pathology in a murine model of lysosomal storage disease. Journal of Inherited Metabolic Disease. 21: 575-86. PMID 9728337 DOI: 10.1023/A:1005423222927 |
0.433 |
|
| 1996 |
Levy B, Galvin N, Vogler C, Birkenmeier EH, Sly WS. Neuropathology of murine mucopolysaccharidosis type VII Acta Neuropathologica. 92: 562-568. PMID 8960313 DOI: 10.1007/S004010050562 |
0.382 |
|
| 1996 |
Vogler C, Sands MS, Levy B, Galvin N, Birkenmeier EH, Sly WS. Enzyme replacement with recombinant beta-glucuronidase in murine mucopolysaccharidosis type VII: impact of therapy during the first six weeks of life on subsequent lysosomal storage, growth, and survival. Pediatric Research. 39: 1050-4. PMID 8725268 DOI: 10.1203/00006450-199606000-00019 |
0.405 |
|
| 1994 |
Vogler C, Sands M, Higgins A, Levy B, Grubb J, Birkenmeier EH, Sly WS. Enzyme replacement with recombinant beta-glucuronidase in the newborn mucopolysaccharidosis type VII mouse. Pediatric Research. 34: 837-40. PMID 8108204 DOI: 10.1203/00006450-199312000-00028 |
0.355 |
|
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