Year |
Citation |
Score |
2014 |
Kan SH, Aoyagi-Scharber M, Le SQ, Vincelette J, Ohmi K, Bullens S, Wendt DJ, Christianson TM, Tiger PM, Brown JR, Lawrence R, Yip BK, Holtzinger J, Bagri A, Crippen-Harmon D, ... ... Neufeld EF, et al. Delivery of an enzyme-IGFII fusion protein to the mouse brain is therapeutic for mucopolysaccharidosis type IIIB. Proceedings of the National Academy of Sciences of the United States of America. 111: 14870-5. PMID 25267636 DOI: 10.1073/Pnas.1416660111 |
0.332 |
|
2014 |
Kan S, Le S, Vincelette J, Bullens S, Brown J, Ohmi K, Lotshaw E, Aoyagi-Scharber M, Crawford BE, Bunting S, Neufeld E, Dickson PI. Intracerebroventricular enzyme replacement therapy with glycosylation-independent lysosomal targeted NAGLU leads to widespread enzymatic activity, reduction of lysosomal storage and of secondary defects in brain of mice with Sanfilippo syndrome type B Molecular Genetics and Metabolism. 111: S59. DOI: 10.1016/J.Ymgme.2013.12.128 |
0.315 |
|
2011 |
Ohmi K, Zhao HZ, Neufeld EF. Defects in the medial entorhinal cortex and dentate gyrus in the mouse model of Sanfilippo syndrome type B Plos One. 6. PMID 22096577 DOI: 10.1371/Journal.Pone.0027461 |
0.3 |
|
2011 |
Neufeld EF. From serendipity to therapy Annual Review of Biochemistry. 80: 1-15. PMID 21675915 DOI: 10.1146/Annurev.Biochem.031209.093756 |
0.302 |
|
2008 |
Chen CHB, Dellamaggiore KR, Ouellette CP, Sedano CD, Lizadjohry M, Chernis GA, Gonzales M, Baltasar FE, Fan AL, Myerowitz R, Neufeld EF. Aptamer-based endocytosis of a lysosomal enzyme Proceedings of the National Academy of Sciences of the United States of America. 105: 15908-15913. PMID 18838694 DOI: 10.1073/Pnas.0808360105 |
0.335 |
|
2007 |
Ryazantsev S, Yu WH, Zhao HZ, Neufeld EF, Ohmi K. Lysosomal accumulation of SCMAS (subunit c of mitochondrial ATP synthase) in neurons of the mouse model of mucopolysaccharidosis III B Molecular Genetics and Metabolism. 90: 393-401. PMID 17185018 DOI: 10.1016/J.Ymgme.2006.11.006 |
0.321 |
|
2006 |
Loewus FA, Kelly S, Neufeld EF. METABOLISM OF MYO-INOSITOL IN PLANTS: CONVERSION TO PECTIN, HEMICELLULOSE, D-XYLOSE, AND SUGAR ACIDS. Proceedings of the National Academy of Sciences of the United States of America. 48: 421-5. PMID 16590933 DOI: 10.1073/Pnas.48.3.421 |
0.32 |
|
2004 |
Zheng Y, Ryazantsev S, Ohmi K, Zhao HZ, Rozengurt N, Kohn DB, Neufeld EF. Retrovirally transduced bone marrow has a therapeutic effect on brain in the mouse model of mucopolysaccharidosis IIIB. Molecular Genetics and Metabolism. 82: 286-95. PMID 15308126 DOI: 10.1016/J.Ymgme.2004.06.004 |
0.305 |
|
2004 |
Zheng Y, Ryazantsev S, Ohmi K, Zhao H, Rozengurt N, Kohn DB, Neufeld EF. 693. Retrovirally Transduced Bone Marrow Has Effect on Brain Pathology in Mouse Model of Mucopolysaccharidosis IIIB Molecular Therapy. 9. DOI: 10.1016/J.Ymthe.2004.06.608 |
0.31 |
|
2003 |
Ohmi K, Greenberg DS, Rajavel KS, Ryazantsev S, Li HH, Neufeld EF. Activated microglia in cortex of mouse models of mucopolysaccharidoses I and IIIB. Proceedings of the National Academy of Sciences of the United States of America. 100: 1902-7. PMID 12576554 DOI: 10.1073/Pnas.252784899 |
0.685 |
|
2002 |
Li HH, Zhao HZ, Neufeld EF, Cai Y, Gómez-Pinilla F. Attenuated plasticity in neurons and astrocytes in the mouse model of Sanfilippo syndrome type B Journal of Neuroscience Research. 69: 30-38. PMID 12111813 DOI: 10.1002/Jnr.10278 |
0.317 |
|
2001 |
Neufeld EF, d'Azzo A. 14. Biosynthesis of normal and mutant β-hexosaminidases Advances in Genetics. 44: 165-171. PMID 11596981 DOI: 10.1016/S0065-2660(01)44078-8 |
0.327 |
|
2001 |
Rajavel KS, Neufeld EF. Nonsense-mediated decay of human HEXA mRNA Molecular and Cellular Biology. 21: 5512-5519. PMID 11463833 DOI: 10.1128/Mcb.21.16.5512-5519.2001 |
0.672 |
|
2001 |
Kakkis ED, Muenzer J, Tiller GE, Waber L, Belmont J, Passage M, Izykowski B, Phillips J, Doroshow R, Walot I, Hoft R, Neufeld EF, Yu KT, Okazaki S, Lewis D, et al. Enzyme-replacement therapy in mucopolysaccharidosis I New England Journal of Medicine. 344: 182-188. PMID 11172140 DOI: 10.1056/Nejm200101183440304 |
0.31 |
|
2000 |
Yu WH, Zhao KW, Ryazantsev S, Rozengurt N, Neufeld EF. Short-term enzyme replacement in the murine model of sanfilippo syndrome type B Molecular Genetics and Metabolism. 71: 573-580. PMID 11136549 DOI: 10.1006/Mgme.2000.3095 |
0.353 |
|
2000 |
Zhao KW, Neufeld EF. Purification and characterization of recombinant human α-N-acetylglucosaminidase secreted by Chinese hamster ovary cells Protein Expression and Purification. 19: 202-211. PMID 10833408 DOI: 10.1006/Prep.2000.1230 |
0.347 |
|
1999 |
Li HH, Yu WH, Rozengurt N, Zhao HZ, Lyons KM, Anagnostaras S, Fanselow MS, Suzuki K, Vanier MT, Neufeld EF. Mouse model of Sanfilippo syndrome type B produced by targeted disruption of the gene encoding alpha-N-acetylglucosaminidase. Proceedings of the National Academy of Sciences of the United States of America. 96: 14505-10. PMID 10588735 DOI: 10.1073/Pnas.96.25.14505 |
0.331 |
|
1998 |
Schmidtchen A, Greenberg D, Zhao HG, Li HH, Huang Y, Tieu P, Zhao HZ, Cheng S, Zhao Z, Whitley CB, Di Natale P, Neufeld EF. NAGLU mutations underlying Sanfilippo syndrome type B American Journal of Human Genetics. 62: 64-69. PMID 9443878 DOI: 10.1086/301685 |
0.333 |
|
1996 |
Kakkis ED, McEntee MF, Schmidtchen A, Neufeld EF, Ward DA, Gompf RE, Kania S, Bedolla C, Chien SL, Shull RM. Long-term and high-dose trials of enzyme replacement therapy in the canine model of mucopolysaccharidosis I. Biochemical and Molecular Medicine. 58: 156-67. PMID 8812735 DOI: 10.1006/Bmme.1996.0044 |
0.32 |
|
1996 |
Zhao HG, Li HH, Bach G, Schmidtchen A, Neufeld EF. The molecular basis of Sanfilippo syndrome type B Proceedings of the National Academy of Sciences of the United States of America. 93: 6101-6105. PMID 8650226 DOI: 10.1073/Pnas.93.12.6101 |
0.32 |
|
1995 |
Tieu PT, Bach G, Matynia A, Hwang M, Neufeld EF. Four novel mutations underlying mild or intermediate forms of alpha-L-iduronidase deficiency (MPS IS and MPS IH/S). Human Mutation. 6: 55-9. PMID 7550232 DOI: 10.1002/Humu.1380060111 |
0.306 |
|
1994 |
Kakkis ED, Matynia A, Jonas AJ, Neufeld EF. Overexpression of the human lysosomal enzyme alpha-L-iduronidase in Chinese hamster ovary cells. Protein Expression and Purification. 5: 225-32. PMID 7950365 DOI: 10.1006/Prep.1994.1035 |
0.322 |
|
1994 |
Shull RM, Kakkis ED, McEntee MF, Kania SA, Jonas AJ, Neufeld EF. Enzyme replacement in a canine model of Hurler syndrome. Proceedings of the National Academy of Sciences of the United States of America. 91: 12937-41. PMID 7809150 DOI: 10.1073/Pnas.91.26.12937 |
0.334 |
|
1983 |
Myerowitz R, Robbins AR, Proia RL, Sahagian GG, Puchalski CM, Neufeld EF. Studies of lysosomal enzyme biosynthesis in cultured cells. Methods in Enzymology. 96: 729-36. PMID 6656651 DOI: 10.1016/S0076-6879(83)96062-7 |
0.315 |
|
1983 |
Spellacy E, Shull RM, Constantopoulos G, Neufeld EF. A canine model of human alpha-L-iduronidase deficiency. Proceedings of the National Academy of Sciences of the United States of America. 80: 6091-5. PMID 6412235 DOI: 10.1073/Pnas.80.19.6091 |
0.312 |
|
1983 |
Bach G, Neufeld EF. Synthesis and maturation of cross-reactive glycoprotein in fibroblasts deficient in arylsulfatase a activity Biochemical and Biophysical Research Communications. 112: 198-205. PMID 6132606 DOI: 10.1016/0006-291X(83)91816-8 |
0.317 |
|
1979 |
Rome LH, Weissmann B, Neufeld EF. Direct demonstration of binding of a lysosomal enzyme, α-L-iduronidase, to receptors on cultured fibroblasts Proceedings of the National Academy of Sciences of the United States of America. 76: 2331-2334. PMID 287076 DOI: 10.1073/Pnas.76.5.2331 |
0.324 |
|
1973 |
Bach G, Eisenberg F, Cantz M, Neufeld EF. The defect in the Hunter syndrome: deficiency of sulfoiduronate sulfatase. Proceedings of the National Academy of Sciences of the United States of America. 70: 2134-8. PMID 4269173 DOI: 10.1073/Pnas.70.7.2134 |
0.338 |
|
1972 |
Bach G, Friedman R, Weissmann B, Neufeld EF. The defect in the Hurler and Scheie syndromes: deficiency of -L-iduronidase Proceedings of the National Academy of Sciences of the United States of America. 69: 2048-2051. PMID 4262258 DOI: 10.1073/Pnas.69.8.2048 |
0.305 |
|
1969 |
Ginsburg V, Neufeld EF. Complex heterosaccharides of animals. Annual Review of Biochemistry. 38: 371-88. PMID 4240949 DOI: 10.1146/annurev.bi.38.070169.002103 |
0.442 |
|
1968 |
Fratantoni JC, Hall CW, Neufeld EF. The defect in Hurler's and Hunter's syndromes: faulty degradation of mucopolysaccharide Proceedings of the National Academy of Sciences of the United States of America. 60: 699-706. PMID 4236091 DOI: 10.1073/Pnas.60.2.699 |
0.304 |
|
1965 |
NEUFELD EF, GINSBURG V. CARBOHYDRATE METABOLISM. Annual Review of Biochemistry. 34: 297-312. PMID 14321172 DOI: 10.1146/annurev.bi.34.070165.001501 |
0.461 |
|
1963 |
Neufeld EF, Hassid WZ. Biosynthesis of Saccharides from Glycopyranosyl Esters of Nucleotides ("Sugar Nucleotides") Advances in Carbohydrate Chemistry. 18: 309-356. PMID 14272320 DOI: 10.1016/S0096-5332(08)60246-5 |
0.485 |
|
1963 |
Frydman RB, Neufeld EF, Hassid WZ. Thymidine diphosphate d-galactose pyrophosphorylase of Phaseolus aureus Bba - Biochimica Et Biophysica Acta. 77: 332-334. PMID 14090450 |
0.487 |
|
1963 |
Feingold DS, Neufeld EF, Hassid WZ. [108] Preparation of UDP-d-xylose and UDP-l-arabinose Methods in Enzymology. 6: 782-787. DOI: 10.1016/0076-6879(63)06248-0 |
0.579 |
|
1961 |
NEUFELD EF, FEINGOLD DS, ILVES SM, KESSLER G, HASSID WZ. Phosphorylation of D-galacturonic acid by extracts from germinating seeds of Phaseolus aureus. The Journal of Biological Chemistry. 236: 3102-5. PMID 14479161 |
0.512 |
|
1961 |
KESSLER G, NEUFELD EF, FEINGOLD DS, HASSID WZ. Metabolism of D-glucuronic acid and D-galacturonic acid by Phaseolus aureus seedlings. The Journal of Biological Chemistry. 236: 308-312. PMID 13752745 |
0.509 |
|
1960 |
NEUFELD EF, FEINGOLD DS, HASSID WZ. Phosphorylation of D-galactose and L-arabinose by extracts from Phaseolus aureus seedlings. The Journal of Biological Chemistry. 235: 906-909. PMID 14426659 |
0.502 |
|
1960 |
FEINGOLD DS, NEUFELD EF, HASSID WZ. The 4-epimerization and decarboxylation of uridine diphosphate D-glucuronic acid by extracts from Phaseolus aureus seedlings. The Journal of Biological Chemistry. 235: 910-3. PMID 13821949 |
0.521 |
|
1959 |
Hassid WZ, Neufeld EF, Feingold DS. SUGAR NUCLEOTIDES IN THE INTERCONVERSION OF CARBOHYDRATES IN HIGHER PLANTS. Proceedings of the National Academy of Sciences of the United States of America. 45: 905-15. PMID 16590482 |
0.467 |
|
1959 |
Neufeld EF, Feingold DS, Hassid WZ. Enzymic phosphorylation of d-glucuronic acid by extracts from seedlings of Phaseolus aureus Archives of Biochemistry and Biophysics. 83: 96-100. PMID 13661996 |
0.537 |
|
1959 |
FEINGOLD DS, NEUFELD EF, HASSID WZ. Xylosyl transfer catalyzed by an asparagus extract. The Journal of Biological Chemistry. 234: 488-489. PMID 13641246 |
0.458 |
|
1958 |
Feingold DS, Neufeld EF, Hassid WZ. Enzymic synthesis of uridine diphosphate glucuronic acid and uridine diphosphate galacturonic acid with extracts from Phaseolus aureus seedlings Archives of Biochemistry and Biophysics. 78: 401-406. PMID 13618023 |
0.526 |
|
1958 |
FEINGOLD DS, NEUFELD EF, HASSID WZ. Synthesis of a beta-1, 3-linked glucan by extracts of Phaseolus aureus seedlings. The Journal of Biological Chemistry. 233: 783-788. PMID 13587492 |
0.478 |
|
1958 |
Neufeld EF, Feingold DS, Hassid WZ. Enzymatic conversion of uridine diphosphate D-glucuronic acid to uridine diphosphate galacturonic acid, uridine diphosphate xylose, and uridine diphosphate arabinose [12] Journal of the American Chemical Society. 80: 4430-4431. |
0.514 |
|
1957 |
Neufeld EF, Ginsburg V, Putman EW, Fanshier D, Hassid WZ. Formation and interconversion of sugar nucleotides by plant extracts Archives of Biochemistry and Biophysics. 69: 602-616. PMID 13445231 |
0.618 |
|
1956 |
Ginsburg V, Neufeld EF, Hassid WZ. ENZYMATIC SYNTHESIS OF URIDINE DIPHOSPHATE XYLOSE AND URIDINE DIPHOSPHATE ARABINOSE. Proceedings of the National Academy of Sciences of the United States of America. 42: 333-5. PMID 16578456 |
0.627 |
|
1955 |
Neufeld EF, Hassid WZ. Hydrolysis of amylose by β-amylase and Z-enzyme Archives of Biochemistry and Biophysics. 59: 405-419. PMID 13275959 |
0.467 |
|
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