Fenfen Wu - Publications

Affiliations: 
Neurology University of Texas Southwestern Medical Center, Dallas, TX, United States 
Area:
muscle channelopathies

27 high-probability publications. We are testing a new system for linking publications to authors. You can help! If you notice any inaccuracies, please sign in and mark papers as correct or incorrect matches. If you identify any major omissions or other inaccuracies in the publication list, please let us know.

Year Citation  Score
2023 Quiñonez M, DiFranco M, Wu F, Cannon SC. Retigabine suppresses loss of force in mouse models of hypokalaemic periodic paralysis. Brain : a Journal of Neurology. PMID 36718088 DOI: 10.1093/brain/awac441  0.633
2022 Wu F, Quiñonez M, Difranco M, Cannon S. CaV1.1 defects in hypokalemic periodic paralysis and harnessing multiple approaches for therapeutic intervention. The Journal of General Physiology. 154. PMID 34767012 DOI: 10.1085/jgp.2021ecc40  0.463
2021 Savalli N, Angelini M, Steccanella F, Wier J, Wu F, Quinonez M, DiFranco M, Neely A, Cannon SC, Olcese R. The distinct role of the four voltage sensors of the skeletal CaV1.1 channel in voltage-dependent activation. The Journal of General Physiology. 153. PMID 34546289 DOI: 10.1085/jgp.202112915  0.668
2021 Wu F, Quinonez M, Cannon SC. Gating pore currents occur in CaV1.1 domain III mutants associated with HypoPP. The Journal of General Physiology. 153. PMID 34463712 DOI: 10.1085/jgp.202112946  0.633
2020 Kubota T, Wu F, Vicart S, Nakaza M, Sternberg D, Watanabe D, Furuta M, Kokunai Y, Abe T, Kokubun N, Fontaine B, Cannon SC, Takahashi MP. Hypokalaemic periodic paralysis with a charge-retaining substitution in the voltage sensor. Brain Communications. 2: fcaa103. PMID 33005891 DOI: 10.1093/braincomms/fcaa103  0.74
2020 Savalli N, Angelini M, Steccanella F, Wu F, Quinonez M, Neely A, Cannon SC, Olcese R. The Contribution of the Individual Voltage Sensors to the Activation of Skeletal CaV1.1 Channels Biophysical Journal. 118: 105a. DOI: 10.1016/J.Bpj.2019.11.728  0.448
2019 Mason ER, Wu F, Patel RR, Xiao Y, Cannon SC, Cummins TR. Resurgent and Gating Pore Currents Induced by de novo Epilepsy Mutations. Eneuro. PMID 31558572 DOI: 10.1523/ENEURO.0141-19.2019  0.662
2019 Mi W, Wu F, Quinonez M, DiFranco M, Cannon SC. Recovery from acidosis is a robust trigger for loss of force in murine hypokalemic periodic paralysis. The Journal of General Physiology. PMID 30733232 DOI: 10.1085/Jgp.201812231  0.647
2019 Savalli N, Wu F, Quinonez M, Cannon SC, Olcese R. A Mutation Linked to Malignant Hyperthermia in the Skeletal CaV1.1 Channel Stabilizes the Resting State of Voltage Sensor I and Impairs Channel Activation Biophysical Journal. 116: 111a. DOI: 10.1016/J.Bpj.2018.11.629  0.683
2018 Wu F, Quinonez M, DiFranco M, Cannon SC. Stac3 enhances expression of human CaV1.1 in Xenopus oocytes and reveals gating pore currents in HypoPP mutant channels. The Journal of General Physiology. PMID 29386226 DOI: 10.1085/Jgp.201711962  0.73
2018 Wu F, Quinonez M, Cannon SC. Gating Pore Currents in DIII Hypopp Mutations of CaV1.1 Biophysical Journal. 114: 639a. DOI: 10.1016/J.Bpj.2017.11.3449  0.443
2018 Savalli N, Wu F, Quinonez M, Cannon SC, Olcese R. Optically-Tracked Structural Rearrangements of the Voltage Sensing Domains in the Human CaV1.1 Channel Biophysical Journal. 114: 39a. DOI: 10.1016/J.Bpj.2017.11.265  0.618
2017 Wu F, Cannon SC. Stac3 Facilitated Expression of Ca V 1.1 in Xenopus Oocytes to Assess Functional Consequences of Hypopp Mutant Ca V 1.1-R528H Biophysical Journal. 112: 245a. DOI: 10.1016/J.Bpj.2016.11.1341  0.327
2016 Wu F, Mi W, Fu Y, Struyk A, Cannon SC. Mice with an NaV1.4 sodium channel null allele have latent myasthenia, without susceptibility to periodic paralysis. Brain : a Journal of Neurology. PMID 27048647 DOI: 10.1093/Brain/Aww070  0.775
2016 Nelson BR, Makarewich CA, Anderson DM, Winders BR, Troupes CD, Wu F, Reese AL, McAnally JR, Chen X, Kavalali ET, Cannon SC, Houser SR, Bassel-Duby R, Olson EN. A peptide encoded by a transcript annotated as long noncoding RNA enhances SERCA activity in muscle. Science (New York, N.Y.). 351: 271-275. PMID 26816378 DOI: 10.1126/Science.Aad4076  0.639
2016 Cannon SC, Mi W, Wu F. Proposed Mechanism for Post‐Exercise Weakness in Hypokalemic Periodic Paralysis The Faseb Journal. 30. DOI: 10.1096/Fasebj.30.1_Supplement.1224.49  0.429
2016 Wu F, Mi W, Fu Y, Cannon SC. Mice with a Null Allele for NaV1.4 Exhibit Pseudo-Myasthenia, but are not Susceptibile to Periodic Paralysis Biophysical Journal. 110: 111a. DOI: 10.1016/J.Bpj.2015.11.656  0.613
2013 Wu F, Mi W, Cannon SC. Beneficial effects of bumetanide in a CaV1.1-R528H mouse model of hypokalaemic periodic paralysis. Brain : a Journal of Neurology. 136: 3766-74. PMID 24142145 DOI: 10.1093/Brain/Awt280  0.734
2013 Nelson BR, Wu F, Liu Y, Anderson DM, McAnally J, Lin W, Cannon SC, Bassel-Duby R, Olson EN. Skeletal muscle-specific T-tubule protein STAC3 mediates voltage-induced Ca2+ release and contractility. Proceedings of the National Academy of Sciences of the United States of America. 110: 11881-6. PMID 23818578 DOI: 10.1073/Pnas.1310571110  0.669
2013 Wu F, Mi W, Cannon SC. Bumetanide prevents transient decreases in muscle force in murine hypokalemic periodic paralysis. Neurology. 80: 1110-6. PMID 23427324 DOI: 10.1212/Wnl.0B013E3182886A0E  0.685
2012 Wu F, Mi W, Hernández-Ochoa EO, Burns DK, Fu Y, Gray HF, Struyk AF, Schneider MF, Cannon SC. A calcium channel mutant mouse model of hypokalemic periodic paralysis. The Journal of Clinical Investigation. 122: 4580-91. PMID 23187123 DOI: 10.1172/Jci66091  0.783
2012 Liu Y, Sugiura Y, Wu F, Mi W, Taketo MM, Cannon S, Carroll T, Lin W. β-Catenin stabilization in skeletal muscles, but not in motor neurons, leads to aberrant motor innervation of the muscle during neuromuscular development in mice. Developmental Biology. 366: 255-67. PMID 22537499 DOI: 10.1016/J.Ydbio.2012.04.003  0.622
2011 Wu F, Mi W, Burns DK, Fu Y, Gray HF, Struyk AF, Cannon SC. A sodium channel knockin mutant (NaV1.4-R669H) mouse model of hypokalemic periodic paralysis. The Journal of Clinical Investigation. 121: 4082-94. PMID 21881211 DOI: 10.1172/Jci57398  0.796
2009 Webb J, Wu FF, Cannon SC. Slow inactivation of the NaV1.4 sodium channel in mammalian cells is impeded by co-expression of the beta1 subunit. Pflã¼Gers Archiv : European Journal of Physiology. 457: 1253-63. PMID 18941776 DOI: 10.1007/S00424-008-0600-8  0.707
2008 Hayward LJ, Kim JS, Lee MY, Zhou H, Kim JW, Misra K, Salajegheh M, Wu FF, Matsuda C, Reid V, Cros D, Hoffman EP, Renaud JM, Cannon SC, Brown RH. Targeted mutation of mouse skeletal muscle sodium channel produces myotonia and potassium-sensitive weakness. The Journal of Clinical Investigation. 118: 1437-49. PMID 18317596 DOI: 10.1172/Jci32638  0.769
2005 Wu FF, Gordon E, Hoffman EP, Cannon SC. A C-terminal skeletal muscle sodium channel mutation associated with myotonia disrupts fast inactivation. The Journal of Physiology. 565: 371-80. PMID 15774523 DOI: 10.1113/Jphysiol.2005.082909  0.709
2002 Wu FF, Ryan A, Devaney J, Warnstedt M, Korade-Mirnics Z, Poser B, Escriva MJ, Pegoraro E, Yee AS, Felice KJ, Giuliani MJ, Mayer RF, Mongini T, Palmucci L, Marino M, et al. Novel CLCN1 mutations with unique clinical and electrophysiological consequences. Brain : a Journal of Neurology. 125: 2392-407. PMID 12390967 DOI: 10.1093/Brain/Awf246  0.459
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