| Year |
Citation |
Score |
| 2023 |
Riddell DO, Hildyard JCW, Harron RCM, Taylor-Brown F, Kornegay JN, Wells DJ, Piercy RJ. Longitudinal assessment of skeletal muscle functional mechanics in the DE50-MD dog model of Duchenne muscular dystrophy. Disease Models & Mechanisms. 16. PMID 38050706 DOI: 10.1242/dmm.050395 |
0.377 |
|
| 2023 |
Birch SM, Lawlor MW, Conlon TJ, Guo LJ, Crudele JM, Hawkins EC, Nghiem PP, Ahn M, Meng H, Beatka MJ, Fickau BA, Prieto JC, Styner MA, Struharik MJ, Shanks C, ... ... Kornegay JN, et al. Assessment of systemic AAV-microdystrophin gene therapy in the GRMD model of Duchenne muscular dystrophy. Science Translational Medicine. 15: eabo1815. PMID 36599002 DOI: 10.1126/scitranslmed.abo1815 |
0.344 |
|
| 2022 |
Schneider SM, Sansom GT, Guo LJ, Furuya S, Weeks BR, Kornegay JN. Natural History of Histopathologic Changes in Cardiomyopathy of Golden Retriever Muscular Dystrophy. Frontiers in Veterinary Science. 8: 759585. PMID 35252412 DOI: 10.3389/fvets.2021.759585 |
0.365 |
|
| 2021 |
Echigoya Y, Trieu N, Duddy W, Moulton HM, Yin H, Partridge TA, Hoffman EP, Kornegay JN, Rohret FA, Rogers CS, Yokota T. A Exon-52 Deleted Miniature Pig Model of Duchenne Muscular Dystrophy and Evaluation of Exon Skipping. International Journal of Molecular Sciences. 22. PMID 34884867 DOI: 10.3390/ijms222313065 |
0.361 |
|
| 2021 |
Martin PT, Zygmunt DA, Ashbrook A, Hamilton S, Packer D, Birch SM, Bettis AK, Balog-Alvarez CJ, Guo LJ, Nghiem PP, Kornegay JN. Short-term treatment of golden retriever muscular dystrophy (GRMD) dogs with rAAVrh74.MHCK7.GALGT2 induces muscle glycosylation and utrophin expression but has no significant effect on muscle strength. Plos One. 16: e0248721. PMID 33770101 DOI: 10.1371/journal.pone.0248721 |
0.386 |
|
| 2020 |
Pryce BR, Labreche C, Hamoudi D, Abou-Hamad J, Al-Zahrani KN, Hodgins JJ, Boulanger-Piette A, Bossé S, Balog-Alvarez C, Frenette J, Ardolino M, Kornegay JN, Sabourin LA. Muscle-Specific Deletion of SLK/Stk2 Enhances p38 Activity and Myogenesis in mdx Mice. Biochimica Et Biophysica Acta. Molecular Cell Research. 118917. PMID 33259860 DOI: 10.1016/j.bbamcr.2020.118917 |
0.379 |
|
| 2020 |
Hawkins EC, Bettis AK, Kornegay JN. Expiratory dysfunction in young dogs with golden retriever muscular dystrophy. Neuromuscular Disorders : Nmd. PMID 33071066 DOI: 10.1016/J.Nmd.2020.09.027 |
0.373 |
|
| 2020 |
López SM, Balog-Alvarez C, Canessa EH, Hathout Y, Brown KJ, Vitha S, Bettis AK, Boehler J, Kornegay JN, Nghiem PP. Creation and characterization of an immortalized canine myoblast cell line: Myok9. Mammalian Genome : Official Journal of the International Mammalian Genome Society. PMID 32246189 DOI: 10.1007/S00335-020-09833-5 |
0.381 |
|
| 2020 |
López SM, Balog-Alvarez C, Vitha S, Bettis AK, Canessa EH, Kornegay JN, Nghiem PP. Challenges associated with homologous directed repair using CRISPR-Cas9 and TALEN to edit the DMD genetic mutation in canine Duchenne muscular dystrophy. Plos One. 15. DOI: 10.1371/Journal.Pone.0228072 |
0.371 |
|
| 2019 |
Song Y, Morales L, Malik AS, Mead AF, Greer CD, Mitchell MA, Petrov MT, Su LT, Choi ME, Rosenblum ST, Lu X, VanBelzen DJ, Krishnankutty RK, Balzer FJ, Loro E, ... ... Kornegay JN, et al. Non-immunogenic utrophin gene therapy for the treatment of muscular dystrophy animal models. Nature Medicine. PMID 31591596 DOI: 10.1038/S41591-019-0594-0 |
0.418 |
|
| 2019 |
Guo LJ, Soslow JH, Bettis AK, Nghiem PP, Cummings KJ, Lenox MW, Miller MW, Kornegay JN, Spurney CF. Natural History of Cardiomyopathy in Adult Dogs With Golden Retriever Muscular Dystrophy. Journal of the American Heart Association. 8: e012443. PMID 31411085 DOI: 10.1161/Jaha.119.012443 |
0.388 |
|
| 2019 |
Eresen A, Hafsa NE, Alic L, Birch SM, Griffin JF, Kornegay JN, Ji JX. Muscle Percentage Index as a Marker of Disease Severity in Golden Retriever Muscular Dystrophy. Muscle & Nerve. PMID 31397906 DOI: 10.1002/Mus.26657 |
0.451 |
|
| 2019 |
Barraza-Flores P, Fontelonga TM, Wuebbles RD, Hermann HJ, Nunes AM, Kornegay JN, Burkin DJ. Laminin-111 protein therapy enhances muscle regeneration and repair in the GRMD dog model of Duchenne muscular dystrophy. Human Molecular Genetics. PMID 31179490 DOI: 10.1093/Hmg/Ddz086 |
0.487 |
|
| 2019 |
Nghiem PP, Kornegay JN. Gene therapies in canine models for Duchenne muscular dystrophy Human Genetics. 138: 483-489. PMID 30734120 DOI: 10.1007/S00439-019-01976-Z |
0.343 |
|
| 2018 |
Eresen A, Alic L, Birch SM, Friedeck W, Griffin JF, Kornegay JN, Ji JX. Texture as an Imaging Biomarker for Disease Severity in Golden Retriever Muscular Dystrophy. Muscle & Nerve. PMID 30461036 DOI: 10.1002/Mus.26386 |
0.352 |
|
| 2018 |
Haddix SG, Lee YI, Kornegay JN, Thompson WJ. Cycles of myofiber degeneration and regeneration lead to remodeling of the neuromuscular junction in two mammalian models of Duchenne muscular dystrophy. Plos One. 13: e0205926. PMID 30379896 DOI: 10.1371/Journal.Pone.0205926 |
0.378 |
|
| 2018 |
Eresen A, Birch SM, Alic L, Griffin Iv JF, Kornegay JN, Ji JX. New Similarity Metric for Registration of MRI to Histology: Golden Retriever Muscular Dystrophy Imaging. Ieee Transactions On Bio-Medical Engineering. PMID 30235115 DOI: 10.1109/Tbme.2018.2870711 |
0.34 |
|
| 2018 |
Mata López S, Hammond JJ, Rigsby MB, Balog-Alvarez CJ, Kornegay JN, Nghiem PP. A novel canine model for Duchenne muscular dystrophy (DMD): single nucleotide deletion in DMD gene exon 20. Skeletal Muscle. 8: 16. PMID 29843823 DOI: 10.1186/S13395-018-0162-1 |
0.482 |
|
| 2018 |
Brinkmeyer-Langford C, Chu C, Balog-Alvarez C, Yu X, Cai JJ, Nabity M, Kornegay JN. Expression profiling of disease progression in canine model of Duchenne muscular dystrophy. Plos One. 13: e0194485. PMID 29554127 DOI: 10.1371/Journal.Pone.0194485 |
0.423 |
|
| 2018 |
Stoughton WB, Li J, Balog-Alvarez C, Kornegay JN. Impaired Autophagy Correlates with Golden Retriever Muscular Dystrophy Phenotype. Muscle & Nerve. PMID 29513363 DOI: 10.1002/Mus.26121 |
0.449 |
|
| 2017 |
Nghiem PP, Bello L, Stoughton WB, López SM, Vidal AH, Hernandez BV, Hulbert KN, Gourley TR, Bettis AK, Balog-Alvarez CJ, Heath-Barnett H, Kornegay JN. Changes in Muscle Metabolism are Associated with Phenotypic Variability in Golden Retriever Muscular Dystrophy
. The Yale Journal of Biology and Medicine. 90: 351-360. PMID 28955176 |
0.351 |
|
| 2017 |
Abdullah M, Kornegay JN, Honcoop A, Parry TL, Balog-Alvarez CJ, O'Neal SK, Bain JR, Muehlbauer MJ, Newgard CB, Patterson C, Willis MS. Non-Targeted Metabolomics Analysis of Golden Retriever Muscular Dystrophy-Affected Muscles Reveals Alterations in Arginine and Proline Metabolism, and Elevations in Glutamic and Oleic Acid In Vivo. Metabolites. 7. PMID 28758940 DOI: 10.3390/Metabo7030038 |
0.463 |
|
| 2017 |
Nghiem PP, Kornegay JN, Uaesoontrachoon K, Bello L, Yin Y, Kesari A, Mittal P, Schatzberg SJ, Many GM, Lee NH, Hoffman EP. Osteopontin is Linked with AKT, FoxO1, and Myostatin in Skeletal Muscle Cells. Muscle & Nerve. PMID 28745831 DOI: 10.1002/Mus.25752 |
0.428 |
|
| 2017 |
Kornegay JN. The Golden Retriever Model of Duchenne Muscular Dystrophy Skeletal Muscle. 7: 9-9. PMID 28526070 DOI: 10.1186/S13395-017-0124-Z |
0.43 |
|
| 2017 |
Markham LW, Brinkmeyer-Langford CL, Soslow JH, Gupte M, Sawyer DB, Kornegay JN, Galindo CL. GRMD cardiac and skeletal muscle metabolism gene profiles are distinct. Bmc Medical Genomics. 10: 21. PMID 28390424 DOI: 10.1186/S12920-017-0257-2 |
0.442 |
|
| 2017 |
VanBelzen DJ, Malik AS, Henthorn PS, Kornegay JN, Stedman HH. Mechanism of Deletion Removing All Dystrophin Exons in a Canine Model for DMD Implicates Concerted Evolution of X Chromosome Pseudogenes. Molecular Therapy. Methods & Clinical Development. 4: 62-71. PMID 28344992 DOI: 10.1016/J.Omtm.2016.12.001 |
0.364 |
|
| 2016 |
Nghiem PP, Bello L, Balog-Alvarez C, López SM, Bettis A, Barnett H, Hernandez B, Schatzberg SJ, Piercy RJ, Kornegay JN. Whole genome sequencing reveals a 7 base-pair deletion in DMD exon 42 in a dog with muscular dystrophy. Mammalian Genome : Official Journal of the International Mammalian Genome Society. PMID 28028563 DOI: 10.1007/S00335-016-9675-2 |
0.357 |
|
| 2016 |
Acosta AR, Van Wie E, Stoughton WB, Bettis AK, Barnett HH, LaBrie NR, Balog-Alvarez CJ, Nghiem PP, Cummings KJ, Kornegay JN. Use of the six-minute walk test to characterize golden retriever muscular dystrophy. Neuromuscular Disorders : Nmd. PMID 27818009 DOI: 10.1016/J.Nmd.2016.09.024 |
0.428 |
|
| 2016 |
Brinkmeyer-Langford C, Balog-Alvarez C, Cai JJ, Davis BW, Kornegay JN. Genome-wide association study to identify potential genetic modifiers in a canine model for Duchenne muscular dystrophy. Bmc Genomics. 17: 665. PMID 27549615 DOI: 10.1186/S12864-016-2948-Z |
0.397 |
|
| 2016 |
Many GM, Yokosaki Y, Uaesoontrachoon K, Nghiem PP, Bello L, Dadgar S, Yin Y, Damsker JM, Cohen HB, Kornegay JN, Bamman MM, Mosser DM, Nagaraju K, Hoffman EP. OPN-a induces muscle inflammation by increasing recruitment and activation of pro-inflammatory macrophages. Experimental Physiology. PMID 27452303 DOI: 10.1113/Ep085768 |
0.408 |
|
| 2016 |
Schneider SM, Coleman AE, Guo LJ, Tou S, Keene BW, Kornegay JN. Suspected acute myocardial infarction in a dystrophin-deficient dog. Neuromuscular Disorders : Nmd. PMID 27105608 DOI: 10.1016/J.Nmd.2016.02.005 |
0.325 |
|
| 2016 |
Kornegay JN, Bogan DJ, Bogan JR, Dow JL, Wang J, Fan Z, Liu N, Warsing LC, Grange RW, Ahn M, Balog-Alvarez CJ, Cotten SW, Willis MS, Brinkmeyer-Langford C, Zhu H, et al. Dystrophin-deficient dogs with reduced myostatin have unequal muscle growth and greater joint contractures. Skeletal Muscle. 6: 14. PMID 27047655 DOI: 10.1186/S13395-016-0085-7 |
0.442 |
|
| 2016 |
Song Y, Malik A, Mead AF, Mitchell M, Petrov M, Su L, Morales L, Rosenblum S, Khurana T, Kornegay JN, Stedman HH. 726. Prevention of Muscular Dystrophy by an AAV Vector Encoding a Nonimmunogenic Protein Based on the Evolution of Utrophin and Dystrophin Molecular Therapy. 24: S286. DOI: 10.1016/S1525-0016(16)33534-1 |
0.417 |
|
| 2016 |
VanBelzen DH, Malik A, Kornegay J, Stedman HH. 627. Concerted Evolution of Pseudogenes Facilitated Contiguous Deletion of the Canine Dystrophin and TMEM47 Genes by Homologous Recombination Molecular Therapy. 24. DOI: 10.1016/S1525-0016(16)33435-9 |
0.349 |
|
| 2016 |
Echigoya Y, Trieu N, Hosoki K, Duddy W, Partridge T, Hoffman E, Kornegay J, Rogers C, Yokota T. 623. Dystrophin Exon 52-Deleted Pigs as a New Animal Model of Duchenne Muscular Dystrophy: Its Characterization and Potential as a Tool for Developing Exon Skipping Therapy Molecular Therapy. 24. DOI: 10.1016/S1525-0016(16)33431-1 |
0.454 |
|
| 2016 |
Song Y, Malik A, Mead A, Mitchell M, Petrov M, Lu X, VanBelzen D, Joffe M, Choi M, Su L, Kornegay J, Khurana TT, Stedman H. 85. AAV9-Utrophin Prevents Myonecrosis in Dystrophic Mice and Dogs without Immunosuppression Molecular Therapy. 24. DOI: 10.1016/S1525-0016(16)32894-5 |
0.454 |
|
| 2015 |
Galindo CL, Soslow JH, Brinkmeyer-Langford CL, Gupte M, Smith HM, Sengsayadeth S, Sawyer DB, Benson DW, Kornegay JN, Markham LW. Translating golden retriever muscular dystrophy microarray findings to novel biomarkers for cardiac/skeletal muscle function in Duchenne Muscular Dystrophy. Pediatric Research. PMID 26672735 DOI: 10.1038/Pr.2015.257 |
0.463 |
|
| 2015 |
Fiorillo AA, Heier CR, Novak JS, Tully CB, Brown KJ, Uaesoontrachoon K, Vila MC, Ngheim PP, Bello L, Kornegay JN, Angelini C, Partridge TA, Nagaraju K, Hoffman EP. TNF-α-Induced microRNAs Control Dystrophin Expression in Becker Muscular Dystrophy. Cell Reports. 12: 1678-90. PMID 26321630 DOI: 10.1016/J.Celrep.2015.07.066 |
0.356 |
|
| 2014 |
Kornegay JN, Peterson JM, Bogan DJ, Kline W, Bogan JR, Dow JL, Fan Z, Wang J, Ahn M, Zhu H, Styner M, Guttridge DC. NBD delivery improves the disease phenotype of the golden retriever model of Duchenne muscular dystrophy. Skeletal Muscle. 4: 18. PMID 25789154 DOI: 10.1186/2044-5040-4-18 |
0.439 |
|
| 2014 |
Kornegay JN, Spurney CF, Nghiem PP, Brinkmeyer-Langford CL, Hoffman EP, Nagaraju K. Pharmacologic management of Duchenne muscular dystrophy: target identification and preclinical trials. Ilar Journal / National Research Council, Institute of Laboratory Animal Resources. 55: 119-49. PMID 24936034 DOI: 10.1093/Ilar/Ilu011 |
0.395 |
|
| 2014 |
Martin PT, Golden B, Okerblom J, Camboni M, Chandrasekharan K, Xu R, Varki A, Flanigan KM, Kornegay JN. A comparative study of N-glycolylneuraminic acid (Neu5Gc) and cytotoxic T cell (CT) carbohydrate expression in normal and dystrophin-deficient dog and human skeletal muscle. Plos One. 9: e88226. PMID 24505439 DOI: 10.1371/Journal.Pone.0088226 |
0.445 |
|
| 2014 |
Mead AF, Petrov M, Malik AS, Mitchell MA, Childers MK, Bogan JR, Seidner G, Kornegay JN, Stedman HH. Diaphragm remodeling and compensatory respiratory mechanics in a canine model of Duchenne muscular dystrophy. Journal of Applied Physiology (Bethesda, Md. : 1985). 116: 807-15. PMID 24408990 DOI: 10.1152/Japplphysiol.00833.2013 |
0.4 |
|
| 2014 |
DeVanna JC, Kornegay JN, Bogan DJ, Bogan JR, Dow JL, Hawkins EC. Respiratory dysfunction in unsedated dogs with golden retriever muscular dystrophy. Neuromuscular Disorders : Nmd. 24: 63-73. PMID 24295812 DOI: 10.1016/J.Nmd.2013.10.001 |
0.329 |
|
| 2014 |
Fan Z, Wang J, Ahn M, Shiloh-Malawsky Y, Chahin N, Elmore S, Bagnell CR, Wilber K, An H, Lin W, Zhu H, Styner M, Kornegay JN. Characteristics of magnetic resonance imaging biomarkers in a natural history study of golden retriever muscular dystrophy. Neuromuscular Disorders : Nmd. 24: 178-91. PMID 24295811 DOI: 10.1016/J.Nmd.2013.10.005 |
0.415 |
|
| 2013 |
Brinkmeyer-Langford C, Kornegay JN. Comparative Genomics of X-linked Muscular Dystrophies: The Golden Retriever Model. Current Genomics. 14: 330-42. PMID 24403852 DOI: 10.2174/13892029113149990004 |
0.379 |
|
| 2013 |
Cotten SW, Kornegay JN, Bogan DJ, Wadosky KM, Patterson C, Willis MS. Genetic myostatin decrease in the golden retriever muscular dystrophy model does not significantly affect the ubiquitin proteasome system despite enhancing the severity of disease. American Journal of Translational Research. 6: 43-53. PMID 24349620 |
0.371 |
|
| 2013 |
Nghiem PP, Hoffman EP, Mittal P, Brown KJ, Schatzberg SJ, Ghimbovschi S, Wang Z, Kornegay JN. Sparing of the dystrophin-deficient cranial sartorius muscle is associated with classical and novel hypertrophy pathways in GRMD dogs American Journal of Pathology. 183: 1411-1424. PMID 24160322 DOI: 10.1016/J.Ajpath.2013.07.013 |
0.426 |
|
| 2013 |
Wuebbles RD, Sarathy A, Kornegay JN, Burkin DJ. Levels of α7 integrin and laminin-α2 are increased following prednisone treatment in the mdx mouse and GRMD dog models of Duchenne muscular dystrophy. Disease Models & Mechanisms. 6: 1175-84. PMID 23846963 DOI: 10.1242/Dmm.012211 |
0.448 |
|
| 2013 |
Wang J, Fan Z, Vandenborne K, Walter G, Shiloh-Malawsky Y, An H, Kornegay JN, Styner MA. A computerized MRI biomarker quantification scheme for a canine model of Duchenne muscular dystrophy. International Journal of Computer Assisted Radiology and Surgery. 8: 763-74. PMID 23299128 DOI: 10.1007/s11548-012-0810-6 |
0.312 |
|
| 2013 |
Barbash IM, Cecchini S, Faranesh AZ, Virag T, Li L, Yang Y, Hoyt RF, Kornegay JN, Bogan JR, Garcia L, Lederman RJ, Kotin RM. MRI roadmap-guided transendocardial delivery of exon-skipping recombinant adeno-associated virus restores dystrophin expression in a canine model of Duchenne muscular dystrophy. Gene Therapy. 20: 274-82. PMID 22551778 DOI: 10.1038/Gt.2012.38 |
0.345 |
|
| 2013 |
Wang J, Fan Z, Vandenborne K, Walter G, Shiloh-Malawsky Y, Ane H, Kornegay JN, Styner MA. Statistical texture analysis based mri quantification of duchenne muscular dystrophy in a canine model Progress in Biomedical Optics and Imaging - Proceedings of Spie. 8672. DOI: 10.1117/12.2006892 |
0.458 |
|
| 2012 |
Sunico SK, Hamel C, Styner M, Robertson ID, Kornegay JN, Bettini C, Parks J, Wilber K, Smallwood JE, Thrall DE. Two anatomic resources of canine pelvic limb muscles based on CT and MRI. Veterinary Radiology & Ultrasound : the Official Journal of the American College of Veterinary Radiology and the International Veterinary Radiology Association. 53: 266-72. PMID 22360713 DOI: 10.1111/J.1740-8261.2012.01926.X |
0.323 |
|
| 2012 |
Kornegay JN, Childers MK, Bogan DJ, Bogan JR, Nghiem P, Wang J, Fan Z, Howard JF, Schatzberg SJ, Dow JL, Grange RW, Styner MA, Hoffman EP, Wagner KR. The paradox of muscle hypertrophy in muscular dystrophy. Physical Medicine and Rehabilitation Clinics of North America. 23: 149-72, xii. PMID 22239881 DOI: 10.1016/J.Pmr.2011.11.014 |
0.488 |
|
| 2012 |
Kornegay JN, Bogan JR, Bogan DJ, Childers MK, Li J, Nghiem P, Detwiler DA, Larsen CA, Grange RW, Bhavaraju-Sanka RK, Tou S, Keene BP, Howard JF, Wang J, Fan Z, et al. Canine models of Duchenne muscular dystrophy and their use in therapeutic strategies. Mammalian Genome : Official Journal of the International Mammalian Genome Society. 23: 85-108. PMID 22218699 DOI: 10.1007/S00335-011-9382-Y |
0.44 |
|
| 2012 |
Bish LT, Sleeper MM, Forbes SC, Wang B, Reynolds C, Singletary GE, Trafny D, Morine KJ, Sanmiguel J, Cecchini S, Virag T, Vulin A, Beley C, Bogan J, Wilson JM, ... ... Kornegay JN, et al. Long-term restoration of cardiac dystrophin expression in golden retriever muscular dystrophy following rAAV6-mediated exon skipping. Molecular Therapy : the Journal of the American Society of Gene Therapy. 20: 580-9. PMID 22146342 DOI: 10.1038/Mt.2011.264 |
0.362 |
|
| 2011 |
Childers MK, Bogan JR, Bogan DJ, Greiner H, Holder M, Grange RW, Kornegay JN. Chronic administration of a leupeptin-derived calpain inhibitor fails to ameliorate severe muscle pathology in a canine model of duchenne muscular dystrophy. Frontiers in Pharmacology. 2: 89. PMID 22291646 DOI: 10.3389/Fphar.2011.00089 |
0.466 |
|
| 2011 |
Wadosky KM, Li L, RodrÃguez JE, Min JN, Bogan D, Gonzalez J, Patterson C, Kornegay JN, Willis M. Regulation of the calpain and ubiquitin-proteasome systems in a canine model of muscular dystrophy. Muscle & Nerve. 44: 553-62. PMID 21826685 DOI: 10.1002/Mus.22125 |
0.392 |
|
| 2011 |
Bish LT, Sleeper MM, Forbes SC, Morine KJ, Reynolds C, Singletary GE, Trafny D, Pham J, Bogan J, Kornegay JN, Vandenborne K, Walter GA, Sweeney HL. Long-term systemic myostatin inhibition via liver-targeted gene transfer in golden retriever muscular dystrophy Human Gene Therapy. 22: 1499-1509. PMID 21787232 DOI: 10.1089/Hum.2011.102 |
0.44 |
|
| 2011 |
Childers MK, Grange RW, Kornegay JN. In vivo canine muscle function assay. Journal of Visualized Experiments : Jove. PMID 21494224 DOI: 10.3791/2623 |
0.425 |
|
| 2011 |
Peterson JM, Kline W, Canan BD, Ricca DJ, Kaspar B, Delfín DA, DiRienzo K, Clemens PR, Robbins PD, Baldwin AS, Flood P, Kaumaya P, Freitas M, Kornegay JN, Mendell JR, et al. Peptide-based inhibition of NF-κB rescues diaphragm muscle contractile dysfunction in a murine model of Duchenne muscular dystrophy. Molecular Medicine (Cambridge, Mass.). 17: 508-15. PMID 21267511 DOI: 10.2119/Molmed.2010.00263 |
0.332 |
|
| 2011 |
Olby NJ, Sharp NJ, Nghiem PE, Keene BW, DeFrancesco TC, Sidley JA, Kornegay JN, Schatzberg SJ. Clinical progression of X-linked muscular dystrophy in two German Shorthaired Pointers. Journal of the American Veterinary Medical Association. 238: 207-12. PMID 21235374 DOI: 10.2460/Javma.238.2.207 |
0.424 |
|
| 2011 |
Miyazato LG, Moraes JRE, Beretta DC, Kornegay JN. Muscular Dystrophy in Dogs Does the Crossing of Breeds Influence Disease Phenotype Veterinary Pathology. 48: 655-662. PMID 21233328 DOI: 10.1177/0300985810387070 |
0.455 |
|
| 2011 |
Kornegay JN, Bogan JR, Bogan DJ, Childers MK, Grange RW. Golden retriever muscular dystrophy (GRMD): Developing and maintaining a colony and physiological functional measurements. Methods in Molecular Biology (Clifton, N.J.). 709: 105-23. PMID 21194024 DOI: 10.1007/978-1-61737-982-6_7 |
0.349 |
|
| 2011 |
Smith BF, Yue Y, Woods PR, Kornegay JN, Shin JH, Williams RR, Duan D. An intronic LINE-1 element insertion in the dystrophin gene aborts dystrophin expression and results in Duchenne-like muscular dystrophy in the corgi breed. Laboratory Investigation; a Journal of Technical Methods and Pathology. 91: 216-31. PMID 20714321 DOI: 10.1038/Labinvest.2010.146 |
0.456 |
|
| 2011 |
Wang J, Fan Z, Kornegay JN, Styner MA. MRI-based quantification of Duchenne muscular dystrophy in a canine model Proceedings of Spie. 7965. DOI: 10.1117/12.878296 |
0.403 |
|
| 2010 |
Tegeler CJ, Grange RW, Bogan DJ, Markert CD, Case D, Kornegay JN, Childers MK. Eccentric contractions induce rapid isometric torque drop in dystrophin-deficient dogs. Muscle & Nerve. 42: 130-2. PMID 20544944 DOI: 10.1002/Mus.21699 |
0.45 |
|
| 2010 |
Kornegay JN, Li J, Bogan JR, Bogan DJ, Chen C, Zheng H, Wang B, Qiao C, Howard JF, Xiao X. Widespread muscle expression of an AAV9 human mini-dystrophin vector after intravenous injection in neonatal dystrophin-deficient dogs. Molecular Therapy : the Journal of the American Society of Gene Therapy. 18: 1501-8. PMID 20517298 DOI: 10.1038/Mt.2010.94 |
0.488 |
|
| 2010 |
Townsend D, Turner I, Yasuda S, Martindale J, Davis J, Shillingford M, Kornegay JN, Metzger JM. Chronic administration of membrane sealant prevents severe cardiac injury and ventricular dilatation in dystrophic dogs. The Journal of Clinical Investigation. 120: 1140-50. PMID 20234088 DOI: 10.1172/Jci41329 |
0.372 |
|
| 2010 |
Pichavant C, Chapdelaine P, Cerri DG, Dominique JC, Quenneville SP, Skuk D, Kornegay JN, Bizario JC, Xiao X, Tremblay JP. Expression of dog microdystrophin in mouse and dog muscles by gene therapy. Molecular Therapy : the Journal of the American Society of Gene Therapy. 18: 1002-9. PMID 20179674 DOI: 10.1038/Mt.2010.23 |
0.484 |
|
| 2010 |
Qiao C, Li J, Zheng H, Bogan J, Li J, Yuan Z, Zhang C, Bogan D, Kornegay J, Xiao X. Hydrodynamic limb vein injection of adeno-associated virus serotype 8 vector carrying canine myostatin propeptide gene into normal dogs enhances muscle growth. Human Gene Therapy. 20: 1-10. PMID 18828709 DOI: 10.1089/Hum.2008.135 |
0.47 |
|
| 2008 |
Yue Y, Ghosh A, Long C, Bostick B, Smith BF, Kornegay JN, Duan D. A single intravenous injection of adeno-associated virus serotype-9 leads to whole body skeletal muscle transduction in dogs. Molecular Therapy : the Journal of the American Society of Gene Therapy. 16: 1944-52. PMID 18827804 DOI: 10.1038/Mt.2008.207 |
0.449 |
|
| 2008 |
Wang B, Li J, Qiao C, Chen C, Hu P, Zhu X, Zhou L, Bogan J, Kornegay J, Xiao X. A canine minidystrophin is functional and therapeutic in mdx mice. Gene Therapy. 15: 1099-106. PMID 18432277 DOI: 10.1038/Gt.2008.70 |
0.402 |
|
| 2008 |
Qiao C, Li J, Zheng H, Bogan J, Li J, Yuan Z, Zhang C, Bogan D, Kornegay J, Xiao X. Hydrodynamic limb vein injection of AAV8 canine myostatin propeptide gene in normal dogs enhances muscle growth Human Gene Therapy. 81015093227032. DOI: 10.1089/Hgt.2008.135 |
0.43 |
|
| 2007 |
Hanft LM, Bogan DJ, Mayer U, Kaufman SJ, Kornegay JN, Ervasti JM. Cytoplasmic gamma-actin expression in diverse animal models of muscular dystrophy. Neuromuscular Disorders : Nmd. 17: 569-74. PMID 17475492 DOI: 10.1016/J.Nmd.2007.03.004 |
0.399 |
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| 2006 |
Brumitt JW, Essman SC, Kornegay JN, Graham JP, Weber WJ, Berry CR. Radiographic features of Golden Retriever muscular dystrophy. Veterinary Radiology & Ultrasound : the Official Journal of the American College of Veterinary Radiology and the International Veterinary Radiology Association. 47: 574-80. PMID 17153067 DOI: 10.1111/J.1740-8261.2006.00188.X |
0.407 |
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| 2006 |
Balzer FJ, Childers MK, Bogan JR, Bogan DJ, Kornegay JN, Stedman HH. 579. Non-Invasive Measurement of Maximal Strength in the Normal and Dystrophic Dog Quadriceps Using Magnetic Stimulation of the Femoral Nerve Molecular Therapy. 13: S223. DOI: 10.1016/J.Ymthe.2006.08.652 |
0.438 |
|
| 2006 |
Smith BF, Kornegay JN. 559. A Pseudo-Exon Derived from an Intronic Insertion Is Responsible for Duchenne-Like Muscular Dystrophy in the Welsh Corgi Dog Molecular Therapy. 13. DOI: 10.1016/J.Ymthe.2006.08.632 |
0.434 |
|
| 2005 |
Han JJ, Carter GT, Weiss MD, Shekar C, Kornegay JN. Using electromyography to assess function in humans and animal models of muscular dystrophy. Physical Medicine and Rehabilitation Clinics of North America. 16: 981-97, x. PMID 16214055 DOI: 10.1016/J.Pmr.2005.08.001 |
0.383 |
|
| 2005 |
Childers MK, Staley JT, Kornegay JN, McDonald KS. Skinned single fibers from normal and dystrophin-deficient dogs incur comparable stretch-induced force deficits. Muscle & Nerve. 31: 768-71. PMID 15736272 DOI: 10.1002/Mus.20298 |
0.309 |
|
| 2005 |
Wang B, Li J, Zhou L, Qiao C, Tian M, Zhu T, Bogan J, Kornegay J, Xiao X. 792. Canine Mini-Dystrophin Gene Transfer by AAV1 in mdx Mice Ameliorates Dystrophic Pathology and Protects Membrane Integrity Molecular Therapy. 11. DOI: 10.1016/J.Ymthe.2005.07.330 |
0.44 |
|
| 2004 |
Liu JM, Okamura CS, Bogan DJ, Bogan JR, Childers MK, Kornegay JN. Effects of prednisone in canine muscular dystrophy. Muscle & Nerve. 30: 767-73. PMID 15468337 DOI: 10.1002/Mus.20154 |
0.385 |
|
| 2004 |
Dell'Agnola C, Wang Z, Storb R, Tapscott SJ, Kuhr CS, Hauschka SD, Lee RS, Sale GE, Zellmer E, Gisburne S, Bogan J, Kornegay JN, Cooper BJ, Gooley TA, Little MT. Hematopoietic stem cell transplantation does not restore dystrophin expression in Duchenne muscular dystrophy dogs. Blood. 104: 4311-8. PMID 15328150 DOI: 10.1182/Blood-2004-06-2247 |
0.41 |
|
| 2003 |
Kornegay JN, Cundiff DD, Bogan DJ, Bogan JR, Okamura CS. The cranial sartorius muscle undergoes true hypertrophy in dogs with golden retriever muscular dystrophy. Neuromuscular Disorders : Nmd. 13: 493-500. PMID 12899877 DOI: 10.1016/S0960-8966(03)00025-7 |
0.435 |
|
| 2002 |
Childers MK, Okamura CS, Bogan DJ, Bogan JR, Petroski GF, McDonald K, Kornegay JN. Eccentric contraction injury in dystrophic canine muscle. Archives of Physical Medicine and Rehabilitation. 83: 1572-8. PMID 12422328 DOI: 10.1053/Apmr.2002.35109 |
0.383 |
|
| 2001 |
Childers MK, Okamura CS, Bogan DJ, Bogan JR, Sullivan MJ, Kornegay JN. Myofiber injury and regeneration in a canine homologue of Duchenne muscular dystrophy American Journal of Physical Medicine and Rehabilitation. 80: 175-181. PMID 11237271 DOI: 10.1097/00002060-200103000-00004 |
0.428 |
|
| 2000 |
Bartlett RJ, Stockinger S, Denis MM, Bartlett WT, Inverardi L, Le TT, thi Man N, Morris GE, Bogan DJ, Metcalf-Bogan J, Kornegay JN. In vivo targeted repair of a point mutation in the canine dystrophin gene by a chimeric RNA/DNA oligonucleotide. Nature Biotechnology. 18: 615-22. PMID 10835598 DOI: 10.1038/76448 |
0.383 |
|
| 1999 |
Kornegay JN, Bogan DJ, Bogan JR, Childers MK, Cundiff DD, Petroski GF, Schueler RO. Contraction force generated by tarsal joint flexion and extension in dogs with golden retriever muscular dystrophy Journal of the Neurological Sciences. 166: 115-121. PMID 10475104 DOI: 10.1016/S0022-510X(99)00118-5 |
0.329 |
|
| 1999 |
Schatzberg SJ, Olby NJ, Breen M, Anderson LV, Langford CF, Dickens HF, Wilton SD, Zeiss CJ, Binns MM, Kornegay JN, Morris GE, Sharp NJ. Molecular analysis of a spontaneous dystrophin 'knockout' dog. Neuromuscular Disorders : Nmd. 9: 289-95. PMID 10407848 DOI: 10.1016/S0960-8966(99)00011-5 |
0.434 |
|
| 1998 |
Schatzberg SJ, Anderson LVB, Wilton SD, Kornegay JN, Mann CJ, Solomon GG, Sharp NJH. Alternative dystrophin gene transcripts in Golden Retriever muscular dystrophy Muscle & Nerve. 21: 991-998. PMID 9655116 DOI: 10.1002/(Sici)1097-4598(199808)21:8<991::Aid-Mus2>3.0.Co;2-0 |
0.434 |
|
| 1996 |
Cauzinille L, Kornegay JN. Fibrocartilaginous embolism of the spinal cord in dogs: review of 36 histologically confirmed cases and retrospective study of 26 suspected cases. Journal of Veterinary Internal Medicine. 10: 241-245. PMID 8819049 DOI: 10.1111/J.1939-1676.1996.Tb02056.X |
0.314 |
|
| 1994 |
Gorospe JR, Tharp MD, Hinckley J, Kornegay JN, Hoffman EP. A role for mast cells in the progression of Duchenne muscular dystrophy? Correlations in dystrophin-deficient humans, dogs, and mice. Journal of the Neurological Sciences. 122: 44-56. PMID 8195802 DOI: 10.1016/0022-510X(94)90050-7 |
0.445 |
|
| 1994 |
Ervasti JM, Roberds SL, Anderson RD, Sharp NJ, Kornegay JN, Campbell KP. Alpha-dystroglycan deficiency correlates with elevated serum creatine kinase and decreased muscle contraction tension in golden retriever muscular dystrophy. Febs Letters. 350: 173-6. PMID 8070559 DOI: 10.1016/0014-5793(94)00748-9 |
0.419 |
|
| 1994 |
Kornegay JN, Sharp NJH, Bogan DJ, Van Camp SD, Metcalf JR, Schueler RO. Contraction tension and kinetics of the peroneus longus muscle in golden retriever muscular dystrophy Journal of the Neurological Sciences. 123: 100-107. PMID 8064300 DOI: 10.1016/0022-510X(94)90210-0 |
0.45 |
|
| 1994 |
Prattis SM, Horton SB, Camp SDv, Kornegay JN. Immunohistochemical detection of neural cell adhesion molecule and laminin in x-linked dystrophic dogs and mdx mice Journal of Comparative Pathology. 110: 253-266. PMID 8040390 DOI: 10.1016/S0021-9975(08)80278-2 |
0.4 |
|
| 1993 |
Sharp NJH, Kornegay JN, Bartlett RJ, Hung W, Dykstra MJ. Notexin-induced muscle injury in the dog. Journal of the Neurological Sciences. 116: 73-81. PMID 8509806 DOI: 10.1016/0022-510X(93)90092-D |
0.394 |
|
| 1993 |
Prattis SM, Gebhart DH, Dickson G, Watt DJ, Kornegay JN. Magnetic Affinity Cell Sorting (MACS) Separation and Flow Cytometric Characterization of Neural Cell Adhesion Molecule-Positive, Cultured Myogenic Cells from Normal and Dystrophic Dogs Experimental Cell Research. 208: 453-464. PMID 8375474 DOI: 10.1006/Excr.1993.1267 |
0.324 |
|
| 1993 |
Hopkins AL, Howard JF, Wheeler SJ, Kornegay JN. Stimulated single fibre electromyography in normal dogs Journal of Small Animal Practice. 34: 271-276. DOI: 10.1111/J.1748-5827.1993.Tb02685.X |
0.434 |
|
| 1992 |
Sharp NJ, Kornegay JN, Van Camp SD, Herbstreith MH, Secore SL, Kettle S, Hung WY, Constantinou CD, Dykstra MJ, Roses AD. An error in dystrophin mRNA processing in golden retriever muscular dystrophy, an animal homologue of Duchenne muscular dystrophy. Genomics. 13: 115-21. PMID 1577476 DOI: 10.1016/0888-7543(92)90210-J |
0.356 |
|
| 1989 |
Kornegay JN, Sharp NJH, Camp SDV, Sussman W. Early Pathologic Features Of Golden Retriever Muscular Dystrophy: A Model Of Duchenne Muscular Dystrophy Journal of Neuropathology and Experimental Neurology. 48: 348. DOI: 10.1097/00005072-198905000-00147 |
0.337 |
|
| 1988 |
Cooper BJ, Winand NJ, Stedman H, Valentine BA, Hoffman EP, Kunkel LM, Scott MO, Fischbeck KH, Kornegay JN, Avery RJ. The homologue of the Duchenne locus is defective in X-linked muscular dystrophy of dogs. Nature. 334: 154-6. PMID 3290691 DOI: 10.1038/334154A0 |
0.421 |
|
| 1988 |
Kornegay JN, Tuler SM, Miller DM, Levesque DC. Muscular dystrophy in a litter of golden retriever dogs Muscle & Nerve. 11: 1056-1064. PMID 3185600 DOI: 10.1002/Mus.880111008 |
0.356 |
|
| 1982 |
Kornegay JN, Gorgacz EJ. Intracranial epidermoid cysts in three dogs. Veterinary Pathology. 19: 646-50. PMID 6983175 DOI: 10.1177/030098588201900608 |
0.308 |
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