Year |
Citation |
Score |
2013 |
Bradbury AM, Cochran JN, McCurdy VJ, Johnson AK, Brunson BL, Gray-Edwards H, Leroy SG, Hwang M, Randle AN, Jackson LS, Morrison NE, Baek RC, Seyfried TN, Cheng SH, Cox NR, et al. Therapeutic response in feline sandhoff disease despite immunity to intracranial gene therapy. Molecular Therapy : the Journal of the American Society of Gene Therapy. 21: 1306-15. PMID 23689599 DOI: 10.1038/Mt.2013.86 |
0.567 |
|
2010 |
Baek RC, Broekman ML, Leroy SG, Tierney LA, Sandberg MA, d'Azzo A, Seyfried TN, Sena-Esteves M. AAV-mediated gene delivery in adult GM1-gangliosidosis mice corrects lysosomal storage in CNS and improves survival. Plos One. 5: e13468. PMID 20976108 DOI: 10.1371/Journal.Pone.0013468 |
0.576 |
|
2010 |
Denny CA, Heinecke KA, Kim YP, Baek RC, Loh KS, Butters TD, Bronson RT, Platt FM, Seyfried TN. Restricted ketogenic diet enhances the therapeutic action of N-butyldeoxynojirimycin towards brain GM2 accumulation in adult Sandhoff disease mice. Journal of Neurochemistry. 113: 1525-35. PMID 20374428 DOI: 10.1111/J.1471-4159.2010.06733.X |
0.565 |
|
2009 |
Baek RC, Martin DR, Cox NR, Seyfried TN. Comparative analysis of brain lipids in mice, cats, and humans with Sandhoff disease. Lipids. 44: 197-205. PMID 19034545 DOI: 10.1007/S11745-008-3268-0 |
0.596 |
|
2009 |
Martin D, Cachon-Gonzalez MB, Sena-Esteves M, Baek RC, Seyfried TN, Cox TM, Cox NR. 84. Adeno-associated virus gene therapy of feline gangliosidosis Molecular Genetics and Metabolism. 96: S30. DOI: 10.1016/j.ymgme.2008.11.085 |
0.428 |
|
2008 |
Mukherjee P, Faber AC, Shelton LM, Baek RC, Chiles TC, Seyfried TN. Thematic review series: sphingolipids. Ganglioside GM3 suppresses the proangiogenic effects of vascular endothelial growth factor and ganglioside GD1a. Journal of Lipid Research. 49: 929-38. PMID 18287616 DOI: 10.1194/Jlr.R800006-Jlr200 |
0.551 |
|
2008 |
Baek RC, Kasperzyk JL, Platt FM, Seyfried TN. N-butyldeoxygalactonojirimycin reduces brain ganglioside and GM2 content in neonatal Sandhoff disease mice. Neurochemistry International. 52: 1125-33. PMID 18207611 DOI: 10.1016/J.Neuint.2007.12.001 |
0.608 |
|
2007 |
McNally MA, Baek RC, Avila RL, Seyfried TN, Strichartz GR, Kirschner DA. Peripheral nervous system manifestations in a Sandhoff disease mouse model: nerve conduction, myelin structure, lipid analysis. Journal of Negative Results in Biomedicine. 6: 8. PMID 17623103 DOI: 10.1186/1477-5751-6-8 |
0.547 |
|
2007 |
Lee JP, Jeyakumar M, Gonzalez R, Takahashi H, Lee PJ, Baek RC, Clark D, Rose H, Fu G, Clarke J, McKercher S, Meerloo J, Muller FJ, Park KI, Butters TD, et al. Stem cells act through multiple mechanisms to benefit mice with neurodegenerative metabolic disease. Nature Medicine. 13: 439-47. PMID 17351625 DOI: 10.1038/Nm1548 |
0.536 |
|
2007 |
Broekman ML, Baek RC, Comer LA, Fernandez JL, Seyfried TN, Sena-Esteves M. Complete correction of enzymatic deficiency and neurochemistry in the GM1-gangliosidosis mouse brain by neonatal adeno-associated virus-mediated gene delivery. Molecular Therapy : the Journal of the American Society of Gene Therapy. 15: 30-7. PMID 17164772 DOI: 10.1038/Sj.Mt.6300004 |
0.602 |
|
2006 |
Yin X, Baek RC, Kirschner DA, Peterson A, Fujii Y, Nave KA, Macklin WB, Trapp BD. Evolution of a neuroprotective function of central nervous system myelin. The Journal of Cell Biology. 172: 469-78. PMID 16449196 DOI: 10.1083/Jcb.200509174 |
0.305 |
|
2005 |
Avila RL, Inouye H, Baek RC, Yin X, Trapp BD, Feltri ML, Wrabetz L, Kirschner DA. Structure and stability of internodal myelin in mouse models of hereditary neuropathy. Journal of Neuropathology and Experimental Neurology. 64: 976-90. PMID 16254492 DOI: 10.1097/01.Jnen.0000186925.95957.Dc |
0.306 |
|
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