William King Engel, MD - Publications

Neurology University of Southern California, Los Angeles, CA, United States 
neuromuscular diseases

40 high-probability publications. We are testing a new system for linking publications to authors. You can help! If you notice any inaccuracies, please sign in and mark papers as correct or incorrect matches. If you identify any major omissions or other inaccuracies in the publication list, please let us know.

Year Citation  Score
2015 Askanas V, Engel WK, Nogalska A. Sporadic inclusion-body myositis: A degenerative muscle disease associated with aging, impaired muscle protein homeostasis and abnormal mitophagy. Biochimica Et Biophysica Acta. 1852: 633-43. PMID 25241263 DOI: 10.1016/j.bbadis.2014.09.005  0.325
2013 Cacciottolo M, Nogalska A, D'Agostino C, Engel WK, Askanas V. Chaperone-mediated autophagy components are upregulated in sporadic inclusion-body myositis muscle fibres. Neuropathology and Applied Neurobiology. 39: 750-61. PMID 23452232 DOI: 10.1111/Nan.12038  0.413
2011 D'Agostino C, Nogalska A, Cacciottolo M, Engel WK, Askanas V. Abnormalities of NBR1, a novel autophagy-associated protein, in muscle fibers of sporadic inclusion-body myositis. Acta Neuropathologica. 122: 627-36. PMID 21935636 DOI: 10.1007/s00401-011-0874-3  0.318
2011 Nogalska A, D'Agostino C, Engel WK, Askanas V. Novel demonstration of conformationally modified tau in sporadic inclusion-body myositis muscle fibers. Neuroscience Letters. 503: 229-33. PMID 21896314 DOI: 10.1016/j.neulet.2011.08.042  0.312
2011 D'Agostino C, Nogalska A, Engel WK, Askanas V. In sporadic inclusion body myositis muscle fibres TDP-43-positive inclusions are less frequent and robust than p62 inclusions, and are not associated with paired helical filaments. Neuropathology and Applied Neurobiology. 37: 315-20. PMID 20626631 DOI: 10.1111/J.1365-2990.2010.01108.X  0.381
2010 Nogalska A, D'Agostino C, Engel WK, Klein WL, Askanas V. Novel demonstration of amyloid-β oligomers in sporadic inclusion-body myositis muscle fibers. Acta Neuropathologica. 120: 661-6. PMID 20711838 DOI: 10.1007/s00401-010-0737-3  0.32
2010 Yan J, Deng HX, Siddique N, Fecto F, Chen W, Yang Y, Liu E, Donkervoort S, Zheng JG, Shi Y, Ahmeti KB, Brooks B, Engel WK, Siddique T. Frameshift and novel mutations in FUS in familial amyotrophic lateral sclerosis and ALS/dementia. Neurology. 75: 807-14. PMID 20668259 DOI: 10.1212/Wnl.0B013E3181F07E0C  0.4
2009 Askanas V, Engel WK, Nogalska A. Inclusion body myositis: a degenerative muscle disease associated with intra-muscle fiber multi-protein aggregates, proteasome inhibition, endoplasmic reticulum stress and decreased lysosomal degradation. Brain Pathology (Zurich, Switzerland). 19: 493-506. PMID 19563541 DOI: 10.1111/j.1750-3639.2009.00290.x  0.329
2008 Wójcik S, Nogalska A, Engel WK, Askanas V. Myostatin and its precursor protein are increased in the skeletal muscle of patients with Type-II muscle fibre atrophy. Folia Morphologica. 67: 6-12. PMID 18335407  0.317
2007 Wojcik S, Paciello O, Engel WK, Askanas V. G.P.13.15 In sporadic inclusion-body myositis muscle-fiber (s-IBM) cytoplasm, cytochrome C aggregates with α-synuclein and amyloid-β precursor protein (AβPP), but does not activate caspase-3 Neuromuscular Disorders. 17: 853. DOI: 10.1016/J.Nmd.2007.06.307  0.349
2007 Wojcik S, Nogalska A, Engel WK, Askanas V. G.P.3.16 In skeletal muscle of patients with type-II fiber atrophy, myostatin (MSTN) and myostatin precursor protein (MSTN-PP) are both increased Neuromuscular Disorders. 17: 787. DOI: 10.1016/J.Nmd.2007.06.091  0.392
2007 Terracciano C, Nogalska A, Engel WK, Wojcik S, Askanas V. G.O.2 In sporadic inclusion-body myositis (s-IBM) muscle fibers, Parkinson-disease-associated DJ-1 is oxidized and might play a novel pathogenic role Neuromuscular Disorders. 17: 766-767. DOI: 10.1016/J.Nmd.2007.06.023  0.354
2005 Fratta P, Engel WK, McFerrin J, Davies KJ, Lin SW, Askanas V. Proteasome inhibition and aggresome formation in sporadic inclusion-body myositis and in amyloid-beta precursor protein-overexpressing cultured human muscle fibers. The American Journal of Pathology. 167: 517-26. PMID 16049336  0.309
2003 Vattemi G, Engel WK, McFerrin J, Pastorino L, Buxbaum JD, Askanas V. BACE1 and BACE2 in pathologic and normal human muscle. Experimental Neurology. 179: 150-8. PMID 12618121 DOI: 10.1016/S0014-4886(02)00025-0  0.36
2001 Vattemi G, Engel WK, McFerrin J, Buxbaum JD, Pastorino L, Askanas V. Presence of BACE1 and BACE2 in muscle fibres of patients with sporadic inclusion-body myositis. Lancet. 358: 1962-4. PMID 11747923 DOI: 10.1016/S0140-6736(01)06969-0  0.312
2000 Askanas V, Engel WK, Alvarez RB, McFerrin J, Broccolini A. Novel immunolocalization of alpha-synuclein in human muscle of inclusion-body myositis, regenerating and necrotic muscle fibers, and at neuromuscular junctions. Journal of Neuropathology and Experimental Neurology. 59: 592-8. PMID 10901230  0.332
2000 Askanas V, Engel WK, Alvarez RB, Frangione B, Ghiso J, Vidal R. Inclusion body myositis, muscle blood vessel and cardiac amyloidosis, and transthyretin Val122Ile allele. Annals of Neurology. 47: 544-9. PMID 10762172 DOI: 10.1002/1531-8249(200004)47:4<544::Aid-Ana24>3.0.Co;2-D  0.326
1999 McFerrin J, Engel WK, Askanas V. Cultured inclusion-body myositis muscle fibers do not accumulate beta-amyloid precursor protein and can be innervated. Neurology. 53: 2184-7. PMID 10599804  0.313
1999 Broccolini A, Engel WK, Askanas V. Localization of survival motor neuron protein in human apoptotic-like and regenerating muscle fibers, and neuromuscular junctions. Neuroreport. 10: 1637-41. PMID 10501549 DOI: 10.1097/00001756-199906030-00003  0.425
1998 Engel WK. The essentiality of histo- and cytochemical studies of skeletal muscle in the investigation of neuromuscular disease. 1962. Neurology. 51: 655 and 17 pages fol. PMID 9748002  0.305
1997 Askanas V, McFerrin J, Alvarez RB, Baqué S, Engel WK. Beta APP gene transfer into cultured human muscle induces inclusion-body myositis aspects. Neuroreport. 8: 2155-8. PMID 9243602 DOI: 10.1097/00001756-199707070-00012  0.33
1996 Mirabella M, Alvarez RB, Engel WK, Weisgraber KH, Askanas V. Apolipoprotein E and apolipoprotein E messenger RNA in muscle of inclusion body myositis and myopathies. Annals of Neurology. 40: 864-72. PMID 9007091 DOI: 10.1002/ana.410400608  0.333
1995 Askanas V, Engel WK. New advances in the understanding of sporadic inclusion-body myositis and hereditary inclusion-body myopathies. Current Opinion in Rheumatology. 7: 486-96. PMID 8579968 DOI: 10.1097/00002281-199511000-00005  0.387
1994 Sarkozi E, Askanas V, Engel WK. Abnormal accumulation of prion protein mRNA in muscle fibers of patients with sporadic inclusion-body myositis and hereditary inclusion-body myopathy. The American Journal of Pathology. 145: 1280-4. PMID 7992832  0.308
1993 Martinuzzi A, Vergani L, Carrozzo R, Fanin M, Bartoloni L, Angelini C, Askanas V, Engel WK. Expression of muscle-type phosphorylase in innervated and aneural cultured muscle of patients with myophosphorylase deficiency. The Journal of Clinical Investigation. 92: 1774-80. PMID 8408630 DOI: 10.1172/JCI116766  0.309
1993 Sussman MA, Bilak M, Kedes L, Engel WK, Askanas V. Tropomodulin is highly concentrated at the postsynaptic domain of human and rat neuromuscular junctions. Experimental Cell Research. 209: 388-91. PMID 8262158 DOI: 10.1006/Excr.1993.1325  0.352
1992 Serdaroglu P, Askanas V, Engel WK. Immunocytochemical localization of ubiquitin at human neuromuscular junctions. Neuropathology and Applied Neurobiology. 18: 232-6. PMID 1321352 DOI: 10.1111/J.1365-2990.1992.Tb00785.X  0.319
1991 Askanas V, Serdaroglu P, Engel WK, Alvarez RB. Immunolocalization of ubiquitin in muscle biopsies of patients with inclusion body myositis and oculopharyngeal muscular dystrophy. Neuroscience Letters. 130: 73-6. PMID 1660975  0.318
1990 Kobayashi T, Askanas V, Saito K, Engel WK, Ishikawa K. Abnormalities of aneural and innervated cultured muscle fibers from patients with myotonic atrophy (dystrophy). Archives of Neurology. 47: 893-6. PMID 2375697  0.303
1990 Pegolo G, Askanas V, Engel WK. Expression of muscle-specific isozymes of phosphorylase and creatine kinase in human muscle fibers cultured aneurally in serum-free, hormonally/chemically enriched medium. International Journal of Developmental Neuroscience : the Official Journal of the International Society For Developmental Neuroscience. 8: 299-308. PMID 2201169  0.303
1990 Kobayashi T, Askanas V, Engel WK. High Excitability And Remained Slow Calcium Repolarization Components Of Action Potentials In Cultured Human Paramyotonia Congenita Muscle Cells Biomedical Research-Tokyo. 11: 299-305. DOI: 10.2220/Biomedres.11.299  0.326
1989 Tomé FM, Askanas V, Engel WK, Alvarez RB, Lee CS. Nuclear inclusions in innervated cultured muscle fibers from patients with oculopharyngeal muscular dystrophy. Neurology. 39: 926-32. PMID 2544827  0.304
1987 Askanas V, Martinuzzi A, Engel WK, Kobayashi T, Stern LZ, Hsu JD. Accumulation of CK-MM is impaired in innervated and contracting cultured muscle fibers of Duchenne muscular dystrophy patients. Life Sciences. 41: 927-33. PMID 3613854  0.306
1985 Askanas V, Engel WK, Kwan HH, Reddy NB, Husainy T, Carlo J, Siddique T, Schwartzman RJ, Hanna CJ. Autosomal dominant syndrome of lipid neuromyopathy with normal carnitine: successful treatment with long-chain fatty-acid-free diet. Neurology. 35: 66-72. PMID 3966003 DOI: 10.1212/WNL.35.1.66  0.5
1983 Engel WK, Siddique T, Nicoloff JT. Effect on weakness and spasticity in amyotrophic lateral sclerosis of thyrotropin-releasing hormone. Lancet. 2: 73-5. PMID 6134961 DOI: 10.1016/S0140-6736(83)90060-0  0.407
1979 Askanas V, Engel WK, Reddy NB, Barth PG, Bethlem J, Krauss DR, Hibberd ME, Lawrence JV, Carter LS. X-linked recessive congenital muscle fiber hypotrophy with central nuclei: abnormalities of growth and adenylate cyclase in muscle tissue cultures. Archives of Neurology. 36: 604-9. PMID 573609 DOI: 10.1001/Archneur.1979.00500460038003  0.323
1977 Bertorini TE, Brumback RA, Kula RW, Engel WK. Electrophysiologic and histochemical observations in five patients with muscle phosphorylase deficiency (MPD). Transactions of the American Neurological Association. 102: 141-2. PMID 616094  0.301
1977 Meienhofer MC, Askanas V, Proux-Daegelen D, Dreyfus JC, Engel WK. Muscle-type phosphorylase activity present in muscle cells cultured from three patients with myophosphorylase deficiency. Archives of Neurology. 34: 779-81. PMID 588100  0.302
1977 Askanas V, Engel WK, Ringel SP, Bender AN. Acetylcholine receptors of aneurally cultured human and animal muscle. Neurology. 27: 1019-22. PMID 562996 DOI: 10.1212/Wnl.27.11.1019  0.313
1975 Levin BE, Engel WK. Iatrogenic muscle fibrosis. Arm levitation as an initial sign. Jama. 234: 621-4. PMID 126328 DOI: 10.1001/jama.1975.03260190049025  0.309
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