Year |
Citation |
Score |
2023 |
Cracco L, Cali I, Cohen ML, Aslam R, Notari S, Kong Q, Newell KL, Ghetti B, Appleby BS, Gambetti P. Efficient transmission of human prion diseases to a glycan-free prion protein-expressing host. Brain : a Journal of Neurology. PMID 38000783 DOI: 10.1093/brain/awad399 |
0.805 |
|
2023 |
Pritzkow S, Ramirez F, Lyon A, Schulz PE, Appleby B, Moda F, Ramirez S, Notari S, Gambetti P, Soto C. Detection of prions in the urine of patients affected by sporadic Creutzfeldt-Jakob disease. Annals of Clinical and Translational Neurology. PMID 37814583 DOI: 10.1002/acn3.51919 |
0.607 |
|
2020 |
Nemani SK, Xiao X, Cali I, Cracco L, Puoti G, Nigro M, Lavrich J, Bharara Singh A, Appleby BS, Sim VL, Notari S, Surewicz WK, Gambetti P. A novel mechanism of phenotypic heterogeneity in Creutzfeldt-Jakob disease. Acta Neuropathologica Communications. 8: 85. PMID 32560672 DOI: 10.1186/S40478-020-00966-X |
0.811 |
|
2019 |
Camacho MV, Telling G, Kong Q, Gambetti P, Notari S. Role of prion protein glycosylation in replication of human prions by protein misfolding cyclic amplification. Laboratory Investigation; a Journal of Technical Methods and Pathology. PMID 31249376 DOI: 10.1038/S41374-019-0282-1 |
0.689 |
|
2019 |
Cracco L, Xiao X, Nemani SK, Lavrich J, Cali I, Ghetti B, Notari S, Surewicz WK, Gambetti P. Gerstmann-Sträussler-Scheinker disease revisited: accumulation of covalently-linked multimers of internal prion protein fragments. Acta Neuropathologica Communications. 7: 1. PMID 31142381 DOI: 10.1186/S40478-019-0734-2 |
0.777 |
|
2019 |
Cali I, Lavrich J, Moda F, Kofskey D, Nemani SK, Appleby B, Tagliavini F, Soto C, Gambetti P, Notari S. PMCA-replicated PrP in urine of vCJD patients maintains infectivity and strain characteristics of brain PrP: Transmission study. Scientific Reports. 9: 5191. PMID 30914754 DOI: 10.1038/S41598-019-41694-0 |
0.785 |
|
2019 |
Nonno R, Notari S, Di Bari MA, Cali I, Pirisinu L, d'Agostino C, Cracco L, Kofskey D, Vanni I, Lavrich J, Parchi P, Agrimi U, Gambetti P. Variable Protease-Sensitive Prionopathy Transmission to Bank Voles. Emerging Infectious Diseases. 25: 73-81. PMID 30561322 DOI: 10.3201/Eid2501.180807 |
0.808 |
|
2018 |
Nemani SK, Notari S, Cali I, Alvarez VE, Kofskey D, Cohen M, Stern RA, Appleby B, Abrams J, Schonberger L, McKee A, Gambetti P. Co-occurrence of chronic traumatic encephalopathy and prion disease. Acta Neuropathologica Communications. 6: 140. PMID 30563563 DOI: 10.1186/S40478-018-0643-9 |
0.793 |
|
2018 |
Notari S, Appleby BS, Gambetti P. Variably protease-sensitive prionopathy. Handbook of Clinical Neurology. 153: 175-190. PMID 29887135 DOI: 10.1016/B978-0-444-63945-5.00010-6 |
0.711 |
|
2017 |
Cracco L, Notari S, Cali I, Sy MS, Chen SG, Cohen ML, Ghetti B, Appleby BS, Zou WQ, Caughey B, Safar JG, Gambetti P. Novel strain properties distinguishing sporadic prion diseases sharing prion protein genotype and prion type. Scientific Reports. 7: 38280. PMID 28091514 DOI: 10.1038/Srep38280 |
0.809 |
|
2016 |
Umeh CC, Kalakoti P, Greenberg MK, Notari S, Cohen Y, Gambetti P, Oblak AL, Ghetti B, Mari Z. Clinicopathological Correlates in a PRNP P102L Mutation Carrier with Rapidly Progressing Parkinsonism-dystonia. Movement Disorders Clinical Practice. 3: 355-358. PMID 27617269 DOI: 10.1002/Mdc3.12307 |
0.627 |
|
2015 |
Ghoshal N, Perry A, McKeel D, Schmidt RE, Carter D, Norton J, Zou WQ, Xiao X, Puoti G, Notari S, Gambetti P, Morris JC, Cairns NJ. Variably Protease-sensitive Prionopathy in an Apparent Cognitively Normal 93-Year-Old. Alzheimer Disease and Associated Disorders. 29: 173-6. PMID 24845762 DOI: 10.1097/Wad.0000000000000049 |
0.662 |
|
2014 |
Cardone F, Principe S, Schininà ME, Maras B, Capellari S, Parchi P, Notari S, Di Francesco L, Poleggi A, Galeno R, Vinci R, Mellina V, Almonti S, Ladogana A, Pocchiari M. Mutant PrPCJD prevails over wild-type PrPCJD in the brain of V210I and R208H genetic Creutzfeldt-Jakob disease patients. Biochemical and Biophysical Research Communications. 454: 289-94. PMID 25450391 DOI: 10.1016/J.Bbrc.2014.10.051 |
0.761 |
|
2014 |
Notari S, Xiao X, Espinosa JC, Cohen Y, Qing L, Aguilar-Calvo P, Kofskey D, Cali I, Cracco L, Kong Q, Torres JM, Zou W, Gambetti P. Transmission characteristics of variably protease-sensitive prionopathy. Emerging Infectious Diseases. 20: 2006-14. PMID 25418590 DOI: 10.3201/Eid2012.140548 |
0.8 |
|
2014 |
Moda F, Gambetti P, Notari S, Concha-Marambio L, Catania M, Park KW, Maderna E, Suardi S, Haïk S, Brandel JP, Ironside J, Knight R, Tagliavini F, Soto C. Prions in the urine of patients with variant Creutzfeldt-Jakob disease. The New England Journal of Medicine. 371: 530-9. PMID 25099577 DOI: 10.1056/Nejmoa1404401 |
0.672 |
|
2014 |
Cannon A, Bieniek KF, Lin WL, Notari S, Zou WQ, Gambetti P, Pedraza O, Graff-Radford NR, Ferman TJ, Dickson DW. Concurrent variably protease-sensitive prionopathy and amyotrophic lateral sclerosis. Acta Neuropathologica. 128: 313-5. PMID 24928712 DOI: 10.1007/S00401-014-1309-8 |
0.576 |
|
2013 |
Saverioni D, Notari S, Capellari S, Poggiolini I, Giese A, Kretzschmar HA, Parchi P. Analyses of protease resistance and aggregation state of abnormal prion protein across the spectrum of human prions. The Journal of Biological Chemistry. 288: 27972-85. PMID 23897825 DOI: 10.1074/Jbc.M113.477547 |
0.732 |
|
2013 |
Gambetti P, Notari S. Human sporadic prion diseases Prions and Diseases. 2: 59-72. DOI: 10.1007/978-1-4614-5338-3_4 |
0.43 |
|
2012 |
Notari S, Qing L, Pocchiari M, Dagdanova A, Hatcher K, Dogterom A, Groisman JF, Lumholtz IB, Puopolo M, Lasmezas C, Chen SG, Kong Q, Gambetti P. Assessing prion infectivity of human urine in sporadic Creutzfeldt-Jakob disease. Emerging Infectious Diseases. 18: 21-8. PMID 22260924 DOI: 10.3201/Eid1801.110589 |
0.628 |
|
2011 |
Gambetti P, Cali I, Notari S, Kong Q, Zou WQ, Surewicz WK. Molecular biology and pathology of prion strains in sporadic human prion diseases. Acta Neuropathologica. 121: 79-90. PMID 21058033 DOI: 10.1007/S00401-010-0761-3 |
0.78 |
|
2010 |
Parchi P, Cescatti M, Notari S, Schulz-Schaeffer WJ, Capellari S, Giese A, Zou WQ, Kretzschmar H, Ghetti B, Brown P. Agent strain variation in human prion disease: insights from a molecular and pathological review of the National Institutes of Health series of experimentally transmitted disease. Brain : a Journal of Neurology. 133: 3030-42. PMID 20823086 DOI: 10.1093/Brain/Awq234 |
0.798 |
|
2010 |
Zou WQ, Puoti G, Xiao X, Yuan J, Qing L, Cali I, Shimoji M, Langeveld JP, Castellani R, Notari S, Crain B, Schmidt RE, Geschwind M, Dearmond SJ, Cairns NJ, et al. Variably protease-sensitive prionopathy: a new sporadic disease of the prion protein. Annals of Neurology. 68: 162-72. PMID 20695009 DOI: 10.1002/Ana.22094 |
0.791 |
|
2010 |
Dagdanova A, Ilchenko S, Notari S, Yang Q, Obrenovich ME, Hatcher K, McAnulty P, Huang L, Zou W, Kong Q, Gambetti P, Chen SG. Characterization of the prion protein in human urine. The Journal of Biological Chemistry. 285: 30489-95. PMID 20670940 DOI: 10.1074/Jbc.M110.161794 |
0.662 |
|
2010 |
Notari S, Moleres FJ, Hunter SB, Belay ED, Schonberger LB, Cali I, Parchi P, Shieh WJ, Brown P, Zaki S, Zou WQ, Gambetti P. Multiorgan detection and characterization of protease-resistant prion protein in a case of variant CJD examined in the United States. Plos One. 5: e8765. PMID 20098730 DOI: 10.1371/Journal.Pone.0008765 |
0.781 |
|
2009 |
Parchi P, Strammiello R, Notari S, Giese A, Langeveld JP, Ladogana A, Zerr I, Roncaroli F, Cras P, Ghetti B, Pocchiari M, Kretzschmar H, Capellari S. Incidence and spectrum of sporadic Creutzfeldt-Jakob disease variants with mixed phenotype and co-occurrence of PrPSc types: an updated classification. Acta Neuropathologica. 118: 659-71. PMID 19718500 DOI: 10.1007/S00401-009-0585-1 |
0.776 |
|
2009 |
Parchi P, Notari S, Weber P, Schimmel H, Budka H, Ferrer I, Haik S, Hauw JJ, Head MW, Ironside JW, Limido L, Rodriguez A, Ströbel T, Tagliavini F, Kretzschmar HA. Inter-laboratory assessment of PrPSc typing in creutzfeldt-jakob disease: a Western blot study within the NeuroPrion Consortium. Brain Pathology (Zurich, Switzerland). 19: 384-91. PMID 18624793 DOI: 10.1111/J.1750-3639.2008.00187.X |
0.663 |
|
2008 |
Notari S, Strammiello R, Capellari S, Giese A, Cescatti M, Grassi J, Ghetti B, Langeveld JP, Zou WQ, Gambetti P, Kretzschmar HA, Parchi P. Characterization of truncated forms of abnormal prion protein in Creutzfeldt-Jakob disease. The Journal of Biological Chemistry. 283: 30557-65. PMID 18753138 DOI: 10.1074/Jbc.M801877200 |
0.801 |
|
2007 |
Notari S, Capellari S, Langeveld J, Giese A, Strammiello R, Gambetti P, Kretzschmar HA, Parchi P. A refined method for molecular typing reveals that co-occurrence of PrP(Sc) types in Creutzfeldt-Jakob disease is not the rule. Laboratory Investigation; a Journal of Technical Methods and Pathology. 87: 1103-12. PMID 17893675 DOI: 10.1038/Labinvest.3700676 |
0.765 |
|
2005 |
Capellari S, Cardone F, Notari S, Schininà ME, Maras B, Sità D, Baruzzi A, Pocchiari M, Parchi P. Creutzfeldt-Jakob disease associated with the R208H mutation in the prion protein gene. Neurology. 64: 905-7. PMID 15753435 DOI: 10.1212/01.Wnl.0000152837.82388.De |
0.771 |
|
2004 |
Notari S, Capellari S, Giese A, Westner I, Baruzzi A, Ghetti B, Gambetti P, Kretzschmar HA, Parchi P. Effects of different experimental conditions on the PrPSc core generated by protease digestion: implications for strain typing and molecular classification of CJD. The Journal of Biological Chemistry. 279: 16797-804. PMID 14754888 DOI: 10.1074/Jbc.M313220200 |
0.77 |
|
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